MAFFUCCI SYNDROME - REVIEW OF THE LITERATURE AND CASE-REPORT

被引:3
|
作者
UNROE, BJ [1 ]
KISSEL, CG [1 ]
ROSENBERG, JC [1 ]
机构
[1] HUTZEL HOSP,DEPT SURG,PODIATRY SECT,DETROIT,MI 48201
关键词
D O I
10.7547/87507315-82-10-532
中图分类号
R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学(修复外科学)];
学科分类号
摘要
Maffucci's syndrome, a rarely occurring congenital disorder, may present early in life as either a pathologic fracture, an incidental radiographic finding, or primarily as multiple hemangiomas. Patients endure years of orthopedic complications, and are faced with a grim prognosis, with the majority developing either skeletal or extra-skeletal malignancies by the end of their fourth decade.
引用
收藏
页码:532 / 536
页数:5
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