MAFFUCCI SYNDROME - REVIEW OF THE LITERATURE AND CASE-REPORT

被引:3
|
作者
UNROE, BJ [1 ]
KISSEL, CG [1 ]
ROSENBERG, JC [1 ]
机构
[1] HUTZEL HOSP,DEPT SURG,PODIATRY SECT,DETROIT,MI 48201
关键词
D O I
10.7547/87507315-82-10-532
中图分类号
R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学(修复外科学)];
学科分类号
摘要
Maffucci's syndrome, a rarely occurring congenital disorder, may present early in life as either a pathologic fracture, an incidental radiographic finding, or primarily as multiple hemangiomas. Patients endure years of orthopedic complications, and are faced with a grim prognosis, with the majority developing either skeletal or extra-skeletal malignancies by the end of their fourth decade.
引用
收藏
页码:532 / 536
页数:5
相关论文
共 50 条
  • [11] THE SUNCT SYNDROME - CASE-REPORT AND REVIEW OF THE LITERATURE
    WOBER, C
    WOBERBINGOL, C
    WESSELY, P
    [J]. FORTSCHRITTE DER NEUROLOGIE PSYCHIATRIE, 1993, 61 (11) : 378 - 382
  • [12] BOERHAAVES SYNDROME - CASE-REPORT AND REVIEW OF THE LITERATURE
    KLIN, B
    BERLATZKY, Y
    URETZKY, G
    [J]. ISRAEL JOURNAL OF MEDICAL SCIENCES, 1989, 25 (02): : 113 - 115
  • [13] NELSONS SYNDROME - CASE-REPORT AND REVIEW OF LITERATURE
    ULLRICH, I
    LIZARRALDE, G
    [J]. SOUTHERN MEDICAL JOURNAL, 1977, 70 (12) : 1444 - 1446
  • [14] THE HEMIMEDULLARY SYNDROME - CASE-REPORT AND REVIEW OF THE LITERATURE
    MOSSUTOAGATIELLO, L
    KNIAHYNICKI, C
    [J]. JOURNAL OF NEUROLOGY, 1990, 237 (03) : 208 - 212
  • [15] GOLDENHAR SYNDROME - CASE-REPORT WITH REVIEW OF LITERATURE
    SINGH, HB
    GAUDI, SC
    [J]. JOURNAL OF LARYNGOLOGY AND OTOLOGY, 1977, 91 (12): : 1101 - 1106
  • [16] FELTYS SYNDROME - A CASE-REPORT - REVIEW OF LITERATURE
    TREVES, R
    RAYNAL, A
    DUDOGNON, P
    LABROUSSE, C
    DESPROGESGOTTERON, R
    [J]. SEMAINE DES HOPITAUX, 1981, 57 (11-1): : 593 - 597
  • [17] THE RAPUNZEL SYNDROME - A CASE-REPORT AND REVIEW OF THE LITERATURE
    BALIK, E
    ULMAN, I
    TANELI, C
    DEMIRCAN, M
    [J]. EUROPEAN JOURNAL OF PEDIATRIC SURGERY, 1993, 3 (03) : 171 - 173
  • [18] ISAACS SYNDROME - CASE-REPORT AND REVIEW OF LITERATURE
    DASILVA, AB
    HEINRICHJAPP, H
    DEPADUADSALDANHA, A
    GUILHONHENRIQUES, F
    [J]. ARQUIVOS DE NEURO-PSIQUIATRIA, 1977, 35 (02) : 139 - 145
  • [19] GORHAMS SYNDROME - A CASE-REPORT AND REVIEW OF THE LITERATURE
    CHOMA, ND
    BISCOTTI, CV
    BAUER, TW
    MEHTA, AC
    LICATA, AA
    [J]. AMERICAN JOURNAL OF MEDICINE, 1987, 83 (06): : 1151 - 1156
  • [20] THE AASE SYNDROME - CASE-REPORT AND REVIEW OF THE LITERATURE
    MUIS, N
    BEEMER, FA
    VANDIJKEN, P
    KLEPDEPATER, JM
    [J]. EUROPEAN JOURNAL OF PEDIATRICS, 1986, 145 (1-2) : 153 - 157