PERSISTENT MULLERIAN DUCT SYNDROME - A CASE-REPORT

被引:4
|
作者
BUSSLINGER, MIC [1 ]
KUHLMANN, B [1 ]
KAISER, G [1 ]
INAEBNIT, D [1 ]
ZUPPINGER, K [1 ]
机构
[1] INSELSPITAL BERN,MED KINDERKLIN,CH-3010 BERN,SWITZERLAND
关键词
PERSISTENT MULLERIAN DUCT SYNDROME; VAS PRESERVATION; 2ND STAGE OPERATION;
D O I
10.1007/BF02125445
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
The persistent Mullerian duct syndrome is a rare disorder of sexual development. We report on a 4 month-old male who presented with a left-sided inguinal hernia and undescended testes. During the repair of the hernia 2 testes, 1 fallopian tube and an uterus were observed. The clinically suspected diagnosis of hernia uteri syndrome was confirmed by laboratory investigations. At the age of 18 months laparotomy was performed and the 2 fused gonades were descended into the right scrotum.
引用
收藏
页码:S79 / S79
页数:1
相关论文
共 50 条
  • [41] Persistent Mullerian duct syndrome: an update
    Picard, Jean-Yves
    Josso, Nathalie
    REPRODUCTION FERTILITY AND DEVELOPMENT, 2019, 31 (07) : 1240 - 1245
  • [42] A Rare Case of Persistent Mullerian Duct Syndrome and Review of Literature
    Ahadi, Mahsa
    Soleimantabar, Hussein
    Javanmard, Babak
    Zahedifard, Sara
    INTERNATIONAL JOURNAL OF CANCER MANAGEMENT, 2020, 13 (03)
  • [43] The management of the persistent Mullerian duct syndrome
    Shalaby, Mahmoud M.
    Kurkar, Adel
    Zarzour, Mohamed A.
    Faddan, Amr A.
    Khalil, Mahmoud
    Abdelhafez, Mohamed F.
    ARAB JOURNAL OF UROLOGY, 2014, 12 (03) : 239 - 244
  • [44] FAMILIAL PERSISTENT MULLERIAN DUCT SYNDROME
    BEHESHTI, M
    CHURCHILL, BM
    HARDY, BE
    BAILEY, JD
    WEKSBERG, R
    ROGAN, GF
    JOURNAL OF UROLOGY, 1984, 131 (05): : 968 - 969
  • [45] Persistent Mullerian Duct Syndrome: A Case-Based Algorithm
    Meyer, T.
    Adam, P.
    Hoecht, B.
    EUROPEAN JOURNAL OF PEDIATRIC SURGERY, 2010, 20 (03) : 194 - 195
  • [46] Persistent mullerian duct syndrome in a dog
    Szabo, Z.
    Moser, J.
    Vincenti, S.
    SCHWEIZER ARCHIV FUR TIERHEILKUNDE, 2023, 165 (03): : 189 - 192
  • [47] A RARE CASE OF PERSISTENT MULLERIAN DUCT SYNDROME WITH TESTICULAR SEMINOMA
    Ghammem, Nour
    Lasmar, Ines
    Ben Mansour, Hajer
    Bouguerra, Fadoua
    Abdessatar, Ghada
    Mezlini, Amel
    INTERNATIONAL JOURNAL OF GYNECOLOGICAL CANCER, 2023, 33 : A116 - A116
  • [48] FAMILIAL PERSISTENT MULLERIAN DUCT SYNDROME
    SLOAN, WR
    WALSH, PC
    JOURNAL OF UROLOGY, 1976, 115 (04): : 459 - 461
  • [49] PERSISTENT MULLERIAN DUCT SYNDROME IN A GOAT
    HAIBEL, GK
    ROJKO, JL
    VETERINARY PATHOLOGY, 1990, 27 (02) : 135 - 137
  • [50] Laparoscopic removal of a persistent mullerian duct in a male: Case report
    Ng, WT
    EUROPEAN JOURNAL OF PEDIATRIC SURGERY, 2001, 11 (02) : 142 - 142