PERSISTENT MULLERIAN DUCT SYNDROME - A CASE-REPORT

被引:4
|
作者
BUSSLINGER, MIC [1 ]
KUHLMANN, B [1 ]
KAISER, G [1 ]
INAEBNIT, D [1 ]
ZUPPINGER, K [1 ]
机构
[1] INSELSPITAL BERN,MED KINDERKLIN,CH-3010 BERN,SWITZERLAND
关键词
PERSISTENT MULLERIAN DUCT SYNDROME; VAS PRESERVATION; 2ND STAGE OPERATION;
D O I
10.1007/BF02125445
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
The persistent Mullerian duct syndrome is a rare disorder of sexual development. We report on a 4 month-old male who presented with a left-sided inguinal hernia and undescended testes. During the repair of the hernia 2 testes, 1 fallopian tube and an uterus were observed. The clinically suspected diagnosis of hernia uteri syndrome was confirmed by laboratory investigations. At the age of 18 months laparotomy was performed and the 2 fused gonades were descended into the right scrotum.
引用
收藏
页码:S79 / S79
页数:1
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