CONSECUTIVE GLIOBLASTOMA AND B-CELL NON-HODGKINS-LYMPHOMA IN A YOUNG-CHILD WITH VONRECKLINGHAUSENS NEUROFIBROMATOSIS

被引:8
|
作者
UYTTEBROECK, A [1 ]
LEGIUS, E [1 ]
BROCK, P [1 ]
VANDECASSEYE, W [1 ]
CASAER, P [1 ]
CASTEELSVANDAELE, M [1 ]
机构
[1] CATHOLIC UNIV LEUVEN, DEPT PAEDIAT, B-3030 HEVERLEE, BELGIUM
来源
MEDICAL AND PEDIATRIC ONCOLOGY | 1995年 / 24卷 / 01期
关键词
NEUROFIBROMATOSIS; MULTIPLE MALIGNANCIES; CHILDHOOD; NON-HODGKINS LYMPHOMA; GLIOBLASTOMA; TUMOR SUPPRESSOR GENE;
D O I
10.1002/mpo.2950240110
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
A young child with neurofibromatosis type 1 (NF1) is reported who developed two primary malignancies: a glioblastoma, followed 6 months later by an abdominal B cell non-Hodgkin's lymphoma. The child is now 4.5 years off treatment and disease free, but has developed progressive and severe psychomotor retardation as sequelae. The NF1 gene is known to act as a tumor suppressor gene. The possible mechanisms leading to the occurrence of a second primary tumor in this child are discussed. (C) Wiley-Liss, Inc.
引用
收藏
页码:46 / 49
页数:4
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