Axonal prion protein is required for peripheral myelin maintenance

被引:0
|
作者
Juliane Bremer
Frank Baumann
Cinzia Tiberi
Carsten Wessig
Heike Fischer
Petra Schwarz
Andrew D Steele
Klaus V Toyka
Klaus-Armin Nave
Joachim Weis
Adriano Aguzzi
机构
[1] Institute of Neuropathology,Department of Neurology
[2] University Hospital of Zürich,Division of Biology
[3] University of Würzburg,Department of Neurogenetics
[4] California Institute of Technology,undefined
[5] Max-Planck Institute of Experimental Medicine,undefined
[6] Institute of Neuropathology,undefined
[7] Medical Faculty,undefined
[8] Rheinisch-Westfälische Technische Hochschule (RWTH,undefined
[9] ) University Aachen,undefined
来源
Nature Neuroscience | 2010年 / 13卷
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摘要
The signals ensuring maintenance of the myelin sheath on peripheral nerves are distinct from those instructing myelination and are largely unknown. Here, the authors report that neuronal expression and regulated proteolysis of the prion protein are essential for myelin maintenance.
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页码:310 / 318
页数:8
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