A Patient With Erdheim-Chester Disease Presenting With Intestinal Obstruction as the Initial Symptom: A Case Report

被引：1

作者：

Zhou, Xiuzhi ^{[1
]}

Zhai, Duchang ^{[1
]}

Yang, Junlin ^{[1
]}

Shi, Dai ^{[1
]}

Lu, Kuan ^{[1
]}

Cai, Wu ^{[1
]}

Fan, Guohua ^{[1
]}

Ju, Shenghong ^{[2
]}

机构：

[1] Soochow Univ, Affiliated Hosp 2, Dept Radiol, Suzhou, Peoples R China

[2] Southeast Univ, Zhongda Hosp, Dept Radiol, Med Sch, Nanjing, Peoples R China

来源：

FRONTIERS IN ONCOLOGY | 2022年 / 12卷

关键词：

Erdheim-Chester disease; non-Langerhans cell histiocytosis; intestinal obstruction; bone imaging; oncology;

D O I：

10.3389/fonc.2022.849578

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

Erdheim-Chester disease (ECD) is a rare and systemic non-Langerhans cell histiocytosis. Recently, ECD was classified as an inflammatory medullary tumor that affects a diverse group of organ systems. The purpose of this report is to present the radiological features of this disease in a 51-year-old man with intestinal obstruction as the initial presentation. In this case, X-ray computed tomography (CT) and emission computed tomography (ECT) clearly showed lesions in various systems, especially in the skeletal images. The survival benefit of treatment with interferon alpha (IFN-alpha) and BRAF inhibitors is well established, while other treatments focus on symptom relief.

引用

页数：5

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