A Patient With Erdheim-Chester Disease Presenting With Intestinal Obstruction as the Initial Symptom: A Case Report

被引：1
|
作者：
Zhou, Xiuzhi [1 ]
Zhai, Duchang [1 ]
Yang, Junlin [1 ]
Shi, Dai [1 ]
Lu, Kuan [1 ]
Cai, Wu [1 ]
Fan, Guohua [1 ]
Ju, Shenghong [2 ]
机构：
[1] Soochow Univ, Affiliated Hosp 2, Dept Radiol, Suzhou, Peoples R China
[2] Southeast Univ, Zhongda Hosp, Dept Radiol, Med Sch, Nanjing, Peoples R China
来源：
FRONTIERS IN ONCOLOGY | 2022年 / 12卷
关键词：
Erdheim-Chester disease; non-Langerhans cell histiocytosis; intestinal obstruction; bone imaging; oncology;
D O I：
10.3389/fonc.2022.849578
中图分类号：
R73 [肿瘤学];
学科分类号：
100214 ;
摘要：
Erdheim-Chester disease (ECD) is a rare and systemic non-Langerhans cell histiocytosis. Recently, ECD was classified as an inflammatory medullary tumor that affects a diverse group of organ systems. The purpose of this report is to present the radiological features of this disease in a 51-year-old man with intestinal obstruction as the initial presentation. In this case, X-ray computed tomography (CT) and emission computed tomography (ECT) clearly showed lesions in various systems, especially in the skeletal images. The survival benefit of treatment with interferon alpha (IFN-alpha) and BRAF inhibitors is well established, while other treatments focus on symptom relief.
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页数：5
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