Primary pulmonary hypertension. A familial form.

被引:0
|
作者
Scherpereel, A [1 ]
Steenhouwer, F [1 ]
Quandalle, P [1 ]
Dennetiere, S [1 ]
Haftel, Y [1 ]
Declercq, N [1 ]
Demarcq, JM [1 ]
机构
[1] CTR HOSP ROUBAIX,SERV SOINS INTENS CARDIOL,ROUBAIX,FRANCE
关键词
primary pulmonary hypertension; familial form; pregnancy;
D O I
暂无
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
The authors present the case of three young female patients, of the same family, with all quickly fatal Primary Pulmonary Hypertension (PPH). Their clinical signs and paraclinical investigations were suggestive of a PPH and excluded all others causes of Pulmonary Hypertension. These observations recall the possible familial cases of this rare and very severe disease. It emphasizes as well the possible revelation of the disease during or after a pregnancy. So the members of this family, essentially first the young women who wish to have children, need a medical detection.
引用
收藏
页码:409 / 412
页数:4
相关论文
共 50 条
  • [41] Pulmonary hypertension. New treatment concepts
    Larsen, R
    Wilhelm, W
    ANAESTHESIST, 2004, 53 (08): : 687 - 687
  • [42] FAMILIAL PRIMARY PULMONARY-HYPERTENSION - CLINICAL-PATTERNS
    LOYD, JE
    PRIMM, RK
    NEWMAN, JH
    AMERICAN REVIEW OF RESPIRATORY DISEASE, 1984, 129 (01): : 194 - 197
  • [43] Guidelines on the identification and treatment of pulmonary hypertension.
    Galie, Nazzareno
    Hoeper, Marius M.
    Humbert, Marc
    Torbicki, Adam
    Vachiery, Jean-Luc
    Barbera, Joan Albert
    Beghetti, Maurice
    Corris, Paul
    Gaine, Sean
    Gibbs, J. Simon
    Gomez-Sanchez, Miguel Angel
    Jondeau, Guillaume
    Klepetko, Walter
    Opitz, Christian
    Peacock, Andrew
    Rubin, Lewis
    Zellweger, Michael
    Simonneau, Gerald
    Vahanian, Alec
    Auricchio, Angelo
    Bax, Jeroen
    Ceconi, Claudio
    Dean, Veronica
    Filippatos, Gerasimos
    Funck-Brentano, Christian
    Hobbs, Richard
    Kearney, Peter
    McDonagh, Theresa
    McGregor, Keith
    Popescu, Bogdan A.
    Reiner, Zeljko
    Sechtem, Udo
    Sirnes, Per Anton
    Tendera, Michal
    Vardas, Panos
    Widimsky, Petr
    Sechtem, Udo
    Al Attar, Nawwar
    Andreotti, Felicita
    Aschermann, Michael
    Asteggiano, Riccardo
    Benza, Ray
    Berger, Rolf
    Bonnet, Damien
    Delcroix, Marion
    Howard, Luke
    Kitsiou, Anastasia N.
    Lang, Irene
    Maggioni, Aldo
    Nielsen-Kudsk, Jens Erik
    KARDIOLOGIA POLSKA, 2009, 67 (11) : S491 - S544
  • [44] Pulmonary hypertension. What is new in therapy?
    Sommer, N.
    Hecker, M.
    Tello, K.
    Richter, M.
    Liebetrau, C.
    Weigand, M. A.
    Seeger, W.
    Ghofrani, A.
    Gall, H.
    ANAESTHESIST, 2016, 65 (08): : 635 - 650
  • [45] GENETIC-ASPECTS OF FAMILIAL PRIMARY PULMONARY-HYPERTENSION
    NEWMAN, JH
    LOYD, JE
    PRIMM, RK
    AMERICAN REVIEW OF RESPIRATORY DISEASE, 1982, 125 (04): : 132 - 132
  • [46] FAMILIAL PRIMARY PULMONARY-HYPERTENSION - REPORT OF 2 SIBLINGS
    KODAMA, K
    HAMADA, M
    SHIGEMATSU, Y
    SUZUKI, M
    HIWADA, K
    HAYASHI, Y
    HASHIMOTO, H
    HASHIMOTO, H
    SUGITA, A
    JAPANESE JOURNAL OF MEDICINE, 1991, 30 (03) : 273 - 277
  • [47] HETEROGENEITY OF PATHOLOGIC LESIONS IN FAMILIAL PRIMARY PULMONARY-HYPERTENSION
    LOYD, JE
    ATKINSON, JB
    PIETRA, GG
    VIRMANI, R
    NEWMAN, JH
    AMERICAN REVIEW OF RESPIRATORY DISEASE, 1988, 138 (04): : 952 - 957
  • [48] Pulmonary hypertension. Definition and diagnostic classification
    Kovacs G.
    Tröster N.
    Scheidl S.
    Olschewski H.
    Der Pneumologe, 2010, 7 (3): : 165 - 173
  • [49] Therapeutic program of pulmonary hypertension. Comments
    Bara, Christoph
    KARDIOCHIRURGIA I TORAKOCHIRURGIA POLSKA-POLISH JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY, 2010, 7 (04) : 468 - 468
  • [50] Good news about pulmonary hypertension.
    Barberá, JA
    ARCHIVOS DE BRONCONEUMOLOGIA, 2001, 37 (03): : 105 - 107