FAMILIAL PRIMARY PULMONARY-HYPERTENSION - REPORT OF 2 SIBLINGS

被引：0

作者：

KODAMA, K ^{[1
]}

HAMADA, M ^{[1
]}

SHIGEMATSU, Y ^{[1
]}

SUZUKI, M ^{[1
]}

HIWADA, K ^{[1
]}

HAYASHI, Y ^{[1
]}

HASHIMOTO, H ^{[1
]}

SUGITA, A ^{[1
]}

机构：

[1] EHIME UNIV,SCH MED,DEPT INTERNAL MED 2,SHIGENOBU,EHIME 79102,JAPAN

来源：

JAPANESE JOURNAL OF MEDICINE | 1991年 / 30卷 / 03期

关键词：

GENETIC TRANSMISSION; RIGHT-SIDED HEART FAILURE;

D O I：

暂无

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Familial primary pulmonary hypertension was found in two siblings (sister and brother). The woman noted exertional dyspnea at the age of 28 yr. The younger brother noticed exertional dyspnea, cough with bloody sputum and pretibial edema at the age of 38 yr. We diagnosed them as primary pulmonary hypertension as based on hemodynamic and histopathological findings. Regardless of the treatment, both patients died of right-sided heart failure with a short time course. We examined their family members, but there were no other members with primary pulmonary hypertension.

引用

页码：273 / 277

页数：5

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