Management of acute bleeding in a patient with congenital afibrinogenaemia

被引:13
|
作者
Vakalopoulou, S.
Rizopoulou, D.
Zafiriadou, E.
Perifanis, V.
Tziomalos, K.
Lefkou, E.
Hill, M.
Dolan, G.
Garipidou, V.
机构
[1] Aristotle Univ Thessaloniki, Haematol Sect Propedeut 2, Dept Internal Med, Hippokrat Hosp, GR-54006 Thessaloniki, Greece
[2] Hippokrateion Hosp, Radiol Dept 1, Thessaloniki, Greece
[3] Queens Med Ctr, Dept Clin Chem & Haematol, Nottingham NG7 2UH, England
关键词
congenital afibrinogenaemia; fibrinogen; fibrinogen concentrates;
D O I
10.1111/j.1365-2516.2006.01340.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Congenital afibrinogenaemia is a rare bleeding disorder characterized by absence of fibrinogen and varying bleeding tendency. Treatment with fibrinogen concentrates is considered to be the best choice for afibrinogenaemic patients who experience bleeding. We report the case of a 22-year-old Greek patient who presented with large muscular haematomas and was treated with fibrinogen concentrates. The efficacy of this treatment and the problems that arose during his hospitalization are being discussed.
引用
收藏
页码:676 / 678
页数:3
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