Management of acute bleeding in a patient with congenital afibrinogenaemia

被引:13
|
作者
Vakalopoulou, S.
Rizopoulou, D.
Zafiriadou, E.
Perifanis, V.
Tziomalos, K.
Lefkou, E.
Hill, M.
Dolan, G.
Garipidou, V.
机构
[1] Aristotle Univ Thessaloniki, Haematol Sect Propedeut 2, Dept Internal Med, Hippokrat Hosp, GR-54006 Thessaloniki, Greece
[2] Hippokrateion Hosp, Radiol Dept 1, Thessaloniki, Greece
[3] Queens Med Ctr, Dept Clin Chem & Haematol, Nottingham NG7 2UH, England
关键词
congenital afibrinogenaemia; fibrinogen; fibrinogen concentrates;
D O I
10.1111/j.1365-2516.2006.01340.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Congenital afibrinogenaemia is a rare bleeding disorder characterized by absence of fibrinogen and varying bleeding tendency. Treatment with fibrinogen concentrates is considered to be the best choice for afibrinogenaemic patients who experience bleeding. We report the case of a 22-year-old Greek patient who presented with large muscular haematomas and was treated with fibrinogen concentrates. The efficacy of this treatment and the problems that arose during his hospitalization are being discussed.
引用
收藏
页码:676 / 678
页数:3
相关论文
共 50 条
  • [31] MANAGEMENT OF ACUTE VARICEAL BLEEDING
    不详
    LANCET, 1988, 2 (8618): : 999 - 1000
  • [32] PREGNANCY IN CONGENITAL AFIBRINOGENAEMIA - REPORT OF A SUCCESSFUL CASE AND REVIEW OF THE LITERATURE
    GRECH, H
    MAJUMDAR, G
    LAWRIE, AS
    SAVIDGE, GF
    BRITISH JOURNAL OF HAEMATOLOGY, 1991, 78 (04) : 571 - 572
  • [33] Management of pregnant women with congenital bleeding disorders
    Pavord, S.
    HAEMOPHILIA, 2015, 21 : 5 - 5
  • [34] High incidence of intracranial haemorrhage in Egyptian children with congenital afibrinogenaemia
    Abdelwahab, Magy
    de Moerloose, Philippe
    Casini, A.
    HAEMOPHILIA, 2023, 29 (02) : 572 - 577
  • [35] CONGENITAL AFIBRINOGENAEMIA AND SUCCESSFUL PREGNANCY OUTCOME - CASE-REPORT
    TREHAN, AK
    FERGUSSON, ILC
    BRITISH JOURNAL OF OBSTETRICS AND GYNAECOLOGY, 1991, 98 (07): : 722 - 724
  • [36] MANAGEMENT OF GASTROINTESTINAL BLEEDING IN AN ACUTE GASTROINTESTINAL BLEEDING UNIT
    WIRTSCHAFTER, SK
    GASTROENTEROLOGY, 1972, 62 (04) : 864 - +
  • [37] Acute gastrointestinal bleeding in stroke patient
    Brzovic, Z
    Brinar, V
    Malojcic, B
    Papa, J
    COLLEGIUM ANTROPOLOGICUM, 1996, 20 (02) : 445 - 451
  • [38] The Use of Recombinant FXIII in a Major Acute Bleeding Episode of a Patient with Congenital FXIII Deficiency the First Experience
    Boda, Zoltan
    Arokszallasi, Anita
    Kerenyi, Adrienne
    Bereczky, Zsuzsanna
    Muszbek, Laszlo
    Pfliegler, Gyorgy
    Schlammadinger, Agota
    BLOOD, 2014, 124 (21)
  • [39] ACUTE BLEEDING IN A PATIENT WITH AN ANTI-KPB ANTIBODY: MANAGEMENT ISSUES AND CASE REPORT
    Nobre Fernandes, S.
    Bischoff, F.
    Carvalho, M.
    Leite, A.
    Alves, B.
    Koch, C.
    Araujo, F.
    VOX SANGUINIS, 2013, 105 : 214 - 215
  • [40] Management of perioperative bleeding in the renal patient
    Heras Benito, M.
    Sanchez Hernandez, R.
    Fernandez-Reyes, M. J.
    Diez Lobo, A. Isabel
    NEFROLOGIA, 2008, 28 (06): : 593 - 596