Management of acute bleeding in a patient with congenital afibrinogenaemia

被引：13
|
作者：
Vakalopoulou, S.
Rizopoulou, D.
Zafiriadou, E.
Perifanis, V.
Tziomalos, K.
Lefkou, E.
Hill, M.
Dolan, G.
Garipidou, V.
机构：
[1] Aristotle Univ Thessaloniki, Haematol Sect Propedeut 2, Dept Internal Med, Hippokrat Hosp, GR-54006 Thessaloniki, Greece
[2] Hippokrateion Hosp, Radiol Dept 1, Thessaloniki, Greece
[3] Queens Med Ctr, Dept Clin Chem & Haematol, Nottingham NG7 2UH, England
来源：
HAEMOPHILIA | 2006年 / 12卷 / 06期
关键词：
congenital afibrinogenaemia; fibrinogen; fibrinogen concentrates;
D O I：
10.1111/j.1365-2516.2006.01340.x
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Congenital afibrinogenaemia is a rare bleeding disorder characterized by absence of fibrinogen and varying bleeding tendency. Treatment with fibrinogen concentrates is considered to be the best choice for afibrinogenaemic patients who experience bleeding. We report the case of a 22-year-old Greek patient who presented with large muscular haematomas and was treated with fibrinogen concentrates. The efficacy of this treatment and the problems that arose during his hospitalization are being discussed.
引用
收藏
页码：676 / 678
页数：3
相关论文
共 50 条
  • [1] Congenital Afibrinogenaemia: Management of microvascular complications in a patient with a severe bleeding phenotype
    Wharin, S.
    Player, P.
    Gooding, R.
    BRITISH JOURNAL OF HAEMATOLOGY, 2018, 181 : 193 - 194
  • [2] Spontaneous Acute Epidural Haematoma in a Paediatric Patient with Congenital Afibrinogenaemia
    Ocak, U.
    Ocak, P. Eser
    Gungorer, B.
    HONG KONG JOURNAL OF PAEDIATRICS, 2019, 24 (03) : 155 - 157
  • [3] Prenatal and peripartum management of congenital afibrinogenaemia
    Kobayashi, T
    Kanayama, N
    Tokunaga, N
    Asahina, T
    Terao, T
    BRITISH JOURNAL OF HAEMATOLOGY, 2000, 109 (02) : 364 - 366
  • [4] Leg ulcer presenting in a patient with congenital afibrinogenaemia
    Kinebuchi, A
    Ohtsuka, T
    Ishida, S
    Otsuka, S
    Abe, T
    Yamakage, A
    Yamazaki, S
    Nakamura, Y
    Hirota, K
    EUROPEAN JOURNAL OF DERMATOLOGY, 2002, 12 (01) : 70 - 72
  • [5] Multiple Bone Cysts in Patient with Congenital Afibrinogenaemia
    Aytac, S.
    Kuskonmaz, B.
    Caglar, O.
    Gumruk, F.
    Cetin, M.
    HAEMOPHILIA, 2016, 22 : 87 - 88
  • [6] CONGENITAL AFIBRINOGENAEMIA
    DESILVA, CC
    THANABALASUNDARAM, RS
    BRITISH MEDICAL JOURNAL, 1951, 2 (4723): : 86 - 88
  • [7] Congenital afibrinogenaemia in pregnancy
    Mensah, P. K.
    Oppenheimer, C.
    Watson, C.
    Pavord, S.
    HAEMOPHILIA, 2011, 17 (01) : 167 - 168
  • [8] A CASE OF CONGENITAL AFIBRINOGENAEMIA
    PRENTICE, AID
    LANCET, 1951, 260 (JAN27): : 211 - 213
  • [9] Spontaneous intracranial bleeding in two patients with congenital afibrinogenaemia and the role of replacement therapy
    Parameswaran, R
    Dickinson, JP
    De Lord, S
    Keeling, DM
    Colvin, BT
    HAEMOPHILIA, 2000, 6 (06) : 705 - 708
  • [10] Cutaneous manifestations of congenital afibrinogenaemia
    Rupec, RA
    Kind, P
    Ruzicka, T
    BRITISH JOURNAL OF DERMATOLOGY, 1996, 134 (03) : 548 - 550
12345