Intra-amniotic delivery of CFTR expressing adenovirus does not reverse Cystic Fibrosis phenotype in inbred CFTR-knockout mice

被引：0

作者：

Buckley, S. M. K. ^{[1
,2
]}

Waddington, S. N. ^{[1
,2
]}

Jezzard, S. ^{[3
]}

Bergau, A. ^{[3
]}

Themis, M. ^{[4
]}

MacVinish, L. J. ^{[5
]}

Cuthbert, A. W. ^{[5
]}

Colledge, W. H. ^{[6
]}

Coutelle, C. ^{[3
]}

机构：

[1] UCL Royal Free & Univ Coll Med Sch, Dept Haematol, Haemophilia Ctr, London, England

[2] UCL Royal Free & Univ Coll Med Sch, Haemostasis Ctr, London, England

[3] Univ London Imperial Coll Sci Technol & Med, Dept Mol Med, Gene Therapy Res Grp, London, England

[4] Brunel Univ, Div Biosci, Genotoxic Grp, Uxbridge UB8 3PH, Middx, England

[5] Univ Cambridge, Addenbrookes Hosp, Dept Med, Cambridge CB2 2QQ, England

[6] Univ Cambridge, Dept Physiol Dev & Neurosci, Cambridge, England

来源：

HUMAN GENE THERAPY | 2008年 / 19卷 / 04期

关键词：

D O I：

暂无

中图分类号：

Q81 [生物工程学（生物技术）]; Q93 [微生物学];

学科分类号：

071005 ; 0836 ; 090102 ; 100705 ;

摘要：

P60

引用

页码：414 / 414

页数：1

共 26 条

[21] Cystic fibrosis phenotype associated with pancreatic insufficiency does not always reflect the cAMP-dependent chloride conductive pathway defect - Analysis of C225R-CFTR and R1066C-CFTR
Fanen, P
Labarthe, R
Garnier, F
Benharouga, M
Goossens, M
Edelman, A
JOURNAL OF BIOLOGICAL CHEMISTRY, 1997, 272 (48) : 30563 - 30566
[22] Cystic fibrosis lung disease following infection with Pseudomonas aeruginosa in Cftr knockout mice using novel non-invasive direct pulmonary infection technique
Guilbault, C
Martin, P
Houle, D
Boghdady, ML
Guiot, MC
Marion, D
Radzioch, D
LABORATORY ANIMALS, 2005, 39 (03) : 336 - 352
[23] Dysregulation of Pendrin and NBC-e1 and Impaired HCO3- Secretion in the Kidneys of CFTR Knockout Mice: Role in the pathogenesis of metabolic alkalosis in cystic fibrosis
Kia, Mujan Varasteh
Barone, Sharon Lynn
Xu, Jie
Zahedi, Kamyar
Soleimani, Manoocher
FASEB JOURNAL, 2016, 30
[24] Lung pathology in response to repeated exposure to Staphylococcus aureus in congenic residual function cystic fibrosis mice does not increase in response to decreased CFTR levels or increased bacterial load
Davidson, DJ
Webb, S
Teague, P
Govan, JRW
Dorin, JR
PATHOBIOLOGY, 2004, 71 (03) : 152 - 158
[25] Functional IL-10 deficiency in the lung of cystic fibrosis (cftr-/-) and IL-10 knockout mice causes increased expression and function of B7 costimulatory molecules on alveolar macrophages
Soltys, J
Bonfield, T
Chmiel, J
Berger, M
JOURNAL OF IMMUNOLOGY, 2002, 168 (04): : 1903 - 1910
[26] E1- E3- REPLICATION DEFICIENT RECOMBINANT ADENOVIRUS VECTOR CONTAINING THE HUMAN CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR (CFTR) CDNA DOES NOT REPLICATE IN HUMAN RESPIRATORY EPITHELIAL-CELLS
ROSENFELD, M
CHU, CS
SETH, P
JAFFE, HA
BANKS, TC
CRYSTAL, RG
JOURNAL OF CELLULAR BIOCHEMISTRY, 1993, : 251 - 251

← 1 2 3 →