Therapeuticall approach of obesity in Prader-Willi syndrome
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作者:
De Carvalho, Daniel F.
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Univ Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, BrazilUniv Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, Brazil
De Carvalho, Daniel F.
[1
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Cercato, Cintia
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Univ Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, BrazilUniv Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, Brazil
Cercato, Cintia
[1
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Almeida, Madson Q.
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Univ Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, BrazilUniv Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, Brazil
Almeida, Madson Q.
[1
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Mancini, Marcio C.
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Univ Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, BrazilUniv Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, Brazil
Mancini, Marcio C.
[1
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Halpern, Alfredo
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Univ Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, BrazilUniv Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, Brazil
Halpern, Alfredo
[1
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机构:
[1] Univ Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, Brazil
Prader-Willi Syndrome (PWS) is a multisystemic genetic disease characterized by hypotonia, mental retardation, characteristic facial appearance, hyperphagia, and compulsive eating due to hypothalamic dysfunction. PWS is caused by loss of function of genes located in chromosome 15q11-q13, an area subject to genomic imprinting. Obesity is a major cause of increased morbidity and mortality among patients with PWS. The objective of this study was to analyze the therapeutic options available for the treatment of the obesity in PWS including pharmacological and surgical strategies.
机构:
Univ Calif San Francisco, Dept Pediat, Div Med Genet, San Francisco, CA 94143 USAUniv Calif San Francisco, Dept Pediat, Div Med Genet, San Francisco, CA 94143 USA
Cassidy, Suzanne B.
Schwartz, Stuart
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Lab Corp Amer, Dept Cytogenet, Res Triangle Pk, NC USAUniv Calif San Francisco, Dept Pediat, Div Med Genet, San Francisco, CA 94143 USA
Schwartz, Stuart
Miller, Jennifer L.
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Univ Florida, Dept Pediat, Div Endocrinol, Gainesville, FL USAUniv Calif San Francisco, Dept Pediat, Div Med Genet, San Francisco, CA 94143 USA
Miller, Jennifer L.
Driscoll, Daniel J.
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机构:
Univ Florida, Ctr Epigenet, Gainesville, FL USA
Univ Florida, Div Pediat Genet & Metab, Gainesville, FL USAUniv Calif San Francisco, Dept Pediat, Div Med Genet, San Francisco, CA 94143 USA
机构:
Univ Kansas, Med Ctr, Dept Psychiat & Behav Sci, Kansas City, KS 66160 USA
Univ Kansas, Med Ctr, Dept Pediat, Kansas City, KS 66160 USAUniv Kansas, Med Ctr, Dept Psychiat & Behav Sci, Kansas City, KS 66160 USA