Pulmonary involvement in Niemann-Pick disease subtype B: CT findings

被引：28

作者：

Ferretti, GR ^{[1
]}

Lantuejoul, S ^{[1
]}

Brambilla, E ^{[1
]}

Coulomb, M ^{[1
]}

机构：

[1] CHU GRENOBLE, HOP MICHALLON, DEPT PATHOL, F-38043 GRENOBLE, FRANCE

来源：

JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY | 1996年 / 20卷 / 06期

关键词：

Niemann-Pick disease; computed tomography; lungs; diseases;

D O I：

10.1097/00004728-199611000-00023

中图分类号：

R8 [特种医学]; R445 [影像诊断学];

学科分类号：

1002 ; 100207 ; 1009 ;

摘要：

We present a case of Niemann-Pick disease subtype B in which the excessive storage of sphingomyelin within lung interstitium and alveoli produced an infiltrative-lung disease demonstrated on high resolution CT (HRCT). HRCT findings were correlated to pathological features.

引用

页码：990 / 992

页数：3

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