Pulmonary involvement in Niemann-Pick disease subtype B: CT findings

被引:28
|
作者
Ferretti, GR [1 ]
Lantuejoul, S [1 ]
Brambilla, E [1 ]
Coulomb, M [1 ]
机构
[1] CHU GRENOBLE, HOP MICHALLON, DEPT PATHOL, F-38043 GRENOBLE, FRANCE
关键词
Niemann-Pick disease; computed tomography; lungs; diseases;
D O I
10.1097/00004728-199611000-00023
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
We present a case of Niemann-Pick disease subtype B in which the excessive storage of sphingomyelin within lung interstitium and alveoli produced an infiltrative-lung disease demonstrated on high resolution CT (HRCT). HRCT findings were correlated to pathological features.
引用
收藏
页码:990 / 992
页数:3
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