Pulmonary involvement in Niemann-Pick disease subtype B: CT findings

被引:28
|
作者
Ferretti, GR [1 ]
Lantuejoul, S [1 ]
Brambilla, E [1 ]
Coulomb, M [1 ]
机构
[1] CHU GRENOBLE, HOP MICHALLON, DEPT PATHOL, F-38043 GRENOBLE, FRANCE
关键词
Niemann-Pick disease; computed tomography; lungs; diseases;
D O I
10.1097/00004728-199611000-00023
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
We present a case of Niemann-Pick disease subtype B in which the excessive storage of sphingomyelin within lung interstitium and alveoli produced an infiltrative-lung disease demonstrated on high resolution CT (HRCT). HRCT findings were correlated to pathological features.
引用
收藏
页码:990 / 992
页数:3
相关论文
共 50 条
  • [1] Niemann-Pick Disease Subtype B and Pulmonary Involvement
    Sanches, Ines
    Rodrigues, Cidalia
    Teixeira, Fatima
    Martins, Yvette
    CHEST, 2014, 145 (03)
  • [2] Pulmonary Involvement of Niemann-Pick Disease
    Ufuk, Furkan
    RADIOLOGY, 2024, 310 (02)
  • [3] Imaging of pulmonary manifestations in subtype B of Niemann-Pick disease
    Duchateau, F
    Dechambre, S
    Coche, E
    BRITISH JOURNAL OF RADIOLOGY, 2001, 74 (887): : 1059 - 1061
  • [4] Niemann-Pick disease type B: HRCT assessment of pulmonary involvement
    Pereira Freitas, Heloisa Maria
    Mancano, Alexandre Dias
    Rodrigues, Rosana Souza
    Hochhegger, Bruno
    Teixeira e Silva Torres, Pedro Paulo
    Escuissato, Dante
    Araujo Neto, Cesar Augusto
    Marchiori, Edson
    JORNAL BRASILEIRO DE PNEUMOLOGIA, 2017, 43 (06) : 451 - 455
  • [5] Pulmonary involvement in an adult, male affected by type B Niemann-Pick disease
    González-Reimers, E
    Sánchez-Pérez, MJ
    Bonilla-Arjona, A
    Rodríguez-Gaspar, M
    Carrasco-Juan, JL
    Alvarez-Argüelles, H
    Santolaria-Fernández, F
    BRITISH JOURNAL OF RADIOLOGY, 2003, 76 (911): : 838 - 840
  • [6] Clinical findings in Niemann-Pick disease type B
    Müssig, K
    Harzer, K
    Mayrhofer, H
    Krägeloh-Mann, I
    Häring, HU
    Machicao, F
    INTERNAL MEDICINE JOURNAL, 2006, 36 (02) : 135 - U18
  • [7] Liver transplantation in a patient with Niemann-Pick disease and pulmonary involvement
    Mendes, Marina Silveira
    Portela, Flaviana Xavier
    Reis, Ricardo Coelho
    Vieira de Castro, Jose Daniel
    Parente Garcia, Jose Huygens
    Holanda, Marcelo Alcantara
    JORNAL BRASILEIRO DE PNEUMOLOGIA, 2012, 38 (02) : 269 - 271
  • [8] RADIOLOGICAL FINDINGS IN NIEMANN-PICK DISEASE
    LACHMAN, R
    CROCKER, A
    SCHULMAN, J
    STRAND, R
    RADIOLOGY, 1973, 108 (03) : 659 - 664
  • [9] OCULAR FINDINGS IN NIEMANN-PICK DISEASE
    LIBERT, J
    TOUSSAINT, D
    GUISELINGS, R
    AMERICAN JOURNAL OF OPHTHALMOLOGY, 1975, 80 (06) : 991 - 1002
  • [10] Early pulmonary involvement in Niemann-Pick type B disease:: Lung lavage is not useful
    Uyan, ZS
    Karadag, B
    Ersu, R
    Kiyan, G
    Kotiloglu, E
    Sirvanci, S
    Ercan, F
    Dagli, T
    Karakoç, F
    Dagli, E
    PEDIATRIC PULMONOLOGY, 2005, 40 (02) : 169 - 172