Isolated left ventricular arrhythmogenic cardiomyopathy: A case report

被引：4
|
作者：
Barbosa-Barros, Raimundo [1 ]
Perez-Riera, Andres Ricardo [2 ]
de Abreu, Luiz Carlos [2 ]
de Sousa-Rocha, Ricardo Paulo [1 ]
da Costa Lino, Danielli Oliveira [1 ]
Baranchuk, Adrian [3 ]
Zhang, Li [4 ,5 ]
机构：
[1] Hosp Messejana Dr Carlos Alberto Studart Gomes, Coronary Ctr, Fortaleza, Ceara, Brazil
[2] ABC Sch Med, Design Studies & Sci Writing Lab, Sao Paulo, Brazil
[3] Queens Univ, Div Cardiol, Kingston, ON, Canada
[4] Lankenau Med Ctr, Wynnewood, PA USA
[5] Lankenau Inst Med Res, Wynnewood, PA USA
来源：
JOURNAL OF ELECTROCARDIOLOGY | 2017年 / 50卷 / 01期
关键词：
Isolated left ventricular arrhythmogenic cardiomyopathy; Electrocardiogram; Intercalated disc;
D O I：
10.1016/j.jelectrocard.2016.09.003
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Left ventricular involvement in the advanced stage of arrhythmogenic cardiomyopathy (AC) is an evolution of this desmosomopathy. Mutation in intercalated discs explains the phenotypic variability. Abnormal trafficking of the intercalated discs at the site of end-to-end contacts between cardiomyocytes and the canonical Wnt/beta-catenin and Hippo signaling pathways have been implicated. In AC, T-wave inversion in lateral leads is the hallmark of left ventricular (LV) involvement. We herein report a case of isolated LV AC in which the initial ECG has typical features: fragmented QRS (fQRS), Twave inversion (TWI) in lateral leads, and ventricular tachycardia from inferobasal LV wall. (C) 2016 Elsevier Inc. All rights reserved.
引用
收藏
页码：144 / 147
页数：4
相关论文
共 50 条
  • [21] Diagnosis and Prognosis of Arrhythmogenic Left Ventricular Cardiomyopathy
    Corrado, Domenico
    Marra, Martina Perazzolo
    Lazzari, Manuel De
    Cipriani, Alberto
    Zorzi, Alessandro
    JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 2020, 76 (11) : 1387 - 1388
  • [22] Arrhythmogenic Left Ventricular Cardiomyopathy Associated With Noncompaction
    Matsukuma, Seiji
    Eishi, Kiyoyuki
    Hashizume, Koji
    Oshitomi, Takashi
    Ariyoshi, Tsuneo
    Taniguchi, Shinichiro
    Hisatomi, Kazuki
    Hayashi, Tomayoshi
    Abe, Kuniko
    ANNALS OF THORACIC SURGERY, 2010, 90 (06): : 2044 - 2046
  • [23] Arrhythmogenic cardiomyopathy with predominant left ventricular involvement
    Aliyev, Farid
    Turkoglu, Cengizhan
    Celiker, Cengiz
    TURK KARDIYOLOJI DERNEGI ARSIVI-ARCHIVES OF THE TURKISH SOCIETY OF CARDIOLOGY, 2010, 38 (03): : 217 - 221
  • [24] Isolated left ventricular arrhythmogenic dysplasia
    Braga, Carlos Galvao
    Silva, Paulo
    Salgado, Alberto
    Magalhaes, Sonia
    Themudo, Raquel
    EUROPEAN HEART JOURNAL-CARDIOVASCULAR IMAGING, 2014, 15 (08) : 907 - 907
  • [25] Multimodality Imaging in Arrhythmogenic Left Ventricular Cardiomyopathy
    Monda, Emanuele
    Rubino, Marta
    Palmiero, Giuseppe
    Verrillo, Federica
    Lioncino, Michele
    Diana, Gaetano
    Cirillo, Annapaola
    Fusco, Adelaide
    Dongiglio, Francesca
    Caiazza, Martina
    Altobelli, Ippolita
    Mauriello, Alfredo
    Guarnaccia, Natale
    Scatteia, Alessandra
    Cesaro, Arturo
    Pacileo, Giuseppe
    Sarubbi, Berardo
    Frisso, Giulia
    Bauce, Barbara
    D'Andrea, Antonello
    Dellegrottaglie, Santo
    Russo, Maria Giovanna
    Calabro, Paolo
    Limongelli, Giuseppe
    JOURNAL OF CLINICAL MEDICINE, 2023, 12 (04)
  • [26] Pregnancy in Women with Arrhythmogenic Left Ventricular Cardiomyopathy
    Bariani, Riccardo
    Marinas, Maria Bueno
    Rigato, Ilaria
    Veronese, Paola
    Celeghin, Rudy
    Cipriani, Alberto
    Cason, Marco
    Pergola, Valeria
    Mattesi, Giulia
    Deola, Petra
    Zorzi, Alessandro
    Limongelli, Giuseppe
    Iliceto, Sabino
    Corrado, Domenico
    Basso, Cristina
    Pilichou, Kalliopi
    Bauce, Barbara
    JOURNAL OF CLINICAL MEDICINE, 2022, 11 (22)
  • [27] Isolated Left Ventricular Non-Compaction Cardiomyopathy Associated with Ventricular Preexcitation: A Case Report
    Bozic, Ivo
    Fabijanic, Damir
    Carevic, Vedran
    Jurilj, Radoslav
    Zekanovic, Drazen
    Bonacin, Damir
    COLLEGIUM ANTROPOLOGICUM, 2009, 33 (04) : 1415 - 1419
  • [28] Left-sided arrhythmogenic ventricular cardiomyopathy with sudden-death in a young man: A case report
    De Carvalho, L.
    Pozzan, G.
    Monteiro, G.
    Bolfarini, F.
    Penny, R.
    Ciconelli Del Guerra, G.
    VIRCHOWS ARCHIV, 2013, 463 (02) : 194 - 194
  • [29] MRI Findings in Desmoplakin-related Arrhythmogenic Left Ventricular Cardiomyopathy in a Pediatric Patient: A Case Report
    Morcos, George
    Vashist, Sudhir
    Aktay, Recai
    RADIOLOGY-CARDIOTHORACIC IMAGING, 2023, 5 (02):
  • [30] A case of arrhythmogenic right ventricular cardiomyopathy
    Goland, Sorel
    Czer, Lawrence S. C.
    Luthringer, Daniel
    Siegel, Robert J.
    CANADIAN JOURNAL OF CARDIOLOGY, 2008, 24 (01) : 61 - 62
12345