We describe a case of a 17-year-old girl with a mediastinal large B-cell lymphoma with IRF4 rearrangement (LBCL-IRF4r) with an atypical clinical presentation in an unusual location, diagnosed by fine needle biopsy, flow cytometry and FISH. We review the literature and discuss the differential diagnosis, clinical presentation, cytological and immunophenotypical characteristics of this unique case that raises very interesting questions regarding this new entity.
机构:
Fudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Inst Pathol, Shanghai, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Jiang, Xiang-Nan
Yu, Fang
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Zhejiang Univ, Dept Pathol, Affiliated Hosp 1, Hangzhou, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Yu, Fang
Xue, Tian
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机构:
Fudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Inst Pathol, Shanghai, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Xue, Tian
Xia, Qing-Xin
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Zhengzhou Univ, Dept Pathol, Affiliated Canc Hosp, Zhengzhou, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Xia, Qing-Xin
Bai, Qian-Ming
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机构:
Fudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Inst Pathol, Shanghai, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Bai, Qian-Ming
Yu, Bao-Hua
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机构:
Fudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Inst Pathol, Shanghai, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Yu, Bao-Hua
Shui, Ruo-Hong
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机构:
Fudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Inst Pathol, Shanghai, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Shui, Ruo-Hong
Zhou, Xiao-Yan
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机构:
Fudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Inst Pathol, Shanghai, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Zhou, Xiao-Yan
Zhu, Xiong-Zeng
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机构:
Fudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Inst Pathol, Shanghai, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Zhu, Xiong-Zeng
Cao, Jun-Ning
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机构:
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Dept Med Oncol, Shanghai Canc Ctr, Shanghai, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Cao, Jun-Ning
Hong, Xiao-Nan
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机构:
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Dept Med Oncol, Shanghai Canc Ctr, Shanghai, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Hong, Xiao-Nan
Li, Xiao-Qiu
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机构:
Fudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
Fudan Univ, Shanghai Med Coll, Dept Oncol, Shanghai, Peoples R China
Fudan Univ, Inst Pathol, Shanghai, Peoples R China
Fudan Univ, Dept Pathol, Shanghai Canc Ctr, 270 Dongan Rd, Shanghai 200032, Peoples R ChinaFudan Univ, Dept Pathol, Shanghai Canc Ctr, Shanghai, Peoples R China
机构:
Mayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Yuan, Ji
Liu, Hui
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机构:
Xuzhou Med Univ, Affiliated Hosp, Dept Pathol, Xuzhou, Peoples R ChinaMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Liu, Hui
Hu, Shimin
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机构:
Univ Texas MD Anderson Canc Ctr, Dept Hematopathol, Houston, TX 77030 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Hu, Shimin
Miranda, Roberto N.
论文数: 0引用数: 0
h-index: 0
机构:
Univ Texas MD Anderson Canc Ctr, Dept Hematopathol, Houston, TX 77030 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Miranda, Roberto N.
Xu, Xinjie
论文数: 0引用数: 0
h-index: 0
机构:
Mayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Xu, Xinjie
Bayerl, Michael G.
论文数: 0引用数: 0
h-index: 0
机构:
Penn State Hershey Hlth, Med Ctr, Dept Pathol, Hershey, PA 17033 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Bayerl, Michael G.
Artymiuk, Cody J.
论文数: 0引用数: 0
h-index: 0
机构:
Mayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Artymiuk, Cody J.
Berg, Holly
论文数: 0引用数: 0
h-index: 0
机构:
Mayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Univ Minnesota, Dept Lab Med & Pathol, Minneapolis, MN 55455 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Berg, Holly
King, Rebecca L.
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机构:
Mayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
King, Rebecca L.
Shi, Min
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机构:
Mayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Shi, Min
He, Rong
论文数: 0引用数: 0
h-index: 0
机构:
Mayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
He, Rong
Viswanatha, David
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机构:
Mayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Viswanatha, David
Medeiros, L. Jeffrey
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机构:
Univ Texas MD Anderson Canc Ctr, Dept Hematopathol, Houston, TX 77030 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Medeiros, L. Jeffrey
Mcphail, Ellen D.
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机构:
Mayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA
Mayo Clin, Dept Lab Med & Pathol, 200 First St SW, Rochester, MN 55905 USAMayo Clin, Dept Lab Med & Pathol, Div Hematopathol, Rochester, MN 55905 USA