HETEROGENOUS PHENOTYPIC-EXPRESSION OF PLASMA AND PLATELET VONWILLEBRAND-FACTOR IN A PEDIGREE WITH VARIANT TYPE-IIC VONWILLEBRAND-DISEASE

被引:0
|
作者
LEDFORD, MR [1 ]
KENT, JW [1 ]
CIVANTOS, F [1 ]
机构
[1] UNIV MIAMI,SCH MED,DEPT PATHOL,MIAMI,FL 33152
关键词
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1124 / 1124
页数:1
相关论文
共 50 条
  • [41] FIBRINOGEN AUGMENTATION OF ENDOGENOUS PLATELET VONWILLEBRAND-FACTOR SURFACE EXPRESSION
    PARKER, RI
    GRALNICK, HR
    CLINICAL RESEARCH, 1986, 34 (02): : A467 - A467
  • [42] EXPRESSION OF ABNORMAL VONWILLEBRAND-FACTOR BY ENDOTHELIAL-CELLS FROM A PATIENT WITH TYPE-IIA VONWILLEBRAND DISEASE
    LEVENE, RB
    BOOYSE, FM
    CHEDIAK, J
    ZIMMERMAN, TS
    LIVINGSTON, DM
    LYNCH, DC
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1987, 84 (18) : 6550 - 6554
  • [43] HETEROGENEITY OF TYPE-I VONWILLEBRAND DISEASE - EVIDENCE FOR A SUBGROUP WITH AN ABNORMAL VONWILLEBRAND-FACTOR
    MANNUCCI, PM
    LOMBARDI, R
    BADER, R
    VIANELLO, L
    FEDERICI, AB
    SOLINAS, S
    MAZZUCCONI, MG
    MARIANI, G
    BLOOD, 1985, 66 (04) : 796 - 802
  • [44] THE FINE-STRUCTURE OF VONWILLEBRAND-FACTOR MULTIMERS AND TYPE-IIA VONWILLEBRAND DISEASE
    LYNCH, DC
    ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1991, 614 : 138 - 152
  • [45] A NEW CONGENITAL PLATELET ABNORMALITY CHARACTERIZED BY SPONTANEOUS PLATELET-AGGREGATION, ENHANCED VONWILLEBRAND-FACTOR PLATELET INTERACTION, AND THE PRESENCE OF ALL VONWILLEBRAND-FACTOR MULTIMERS IN PLASMA
    CASONATO, A
    DEMARCO, L
    MAZZUCATO, M
    DEANGELIS, V
    DEROIA, D
    FABRIS, F
    RUGGERI, ZM
    GIROLAMI, A
    BLOOD, 1989, 74 (06) : 2028 - 2033
  • [46] IDENTIFICATION OF 2 POINT MUTATIONS IN THE VONWILLEBRAND-FACTOR GENE OF 3 FAMILIES WITH THE NORMANDY VARIANT OF VONWILLEBRAND DISEASE
    GAUCHER, C
    MERCIER, B
    JORIEUX, S
    OUFKIR, D
    MAZURIER, C
    BRITISH JOURNAL OF HAEMATOLOGY, 1991, 78 (04) : 506 - 514
  • [47] MOLECULAR CHARACTERIZATION OF THE BREAKPOINTS IN A HETEROZYGOUS DELETION OF VONWILLEBRAND-FACTOR GENE CAUSING A DOMINANT VARIANT OF VONWILLEBRAND DISEASE
    PATRACCHINI, P
    MARCHETTI, G
    GEMMATI, D
    GUERRA, S
    SCHWIENBACHER, C
    BALLERINI, G
    BERNARDI, F
    AMERICAN JOURNAL OF HUMAN GENETICS, 1991, 49 (04) : 94 - 94
  • [48] VONWILLEBRANDS DISEASE WITH SPONTANEOUS PLATELET-AGGREGATION INDUCED BY AN ABNORMAL PLASMA VONWILLEBRAND-FACTOR
    GRALNICK, HR
    WILLIAMS, SB
    MCKEOWN, LP
    RICK, ME
    MAISONNEUVE, P
    JENNEAU, C
    SULTAN, Y
    JOURNAL OF CLINICAL INVESTIGATION, 1985, 76 (04): : 1522 - 1529
  • [49] PLATELET-AGGREGATION INDUCED BY TYPE-IIB PLATELET VONWILLEBRAND-FACTOR
    GRALNICK, HR
    MCKEOWN, LP
    WILLIAMS, S
    JENNEAU, C
    SULTAN, Y
    VANMOURIK, J
    BRITISH JOURNAL OF HAEMATOLOGY, 1989, 71 (02) : 253 - 258
  • [50] ROLE OF PLASMA AND PLATELET VONWILLEBRAND-FACTOR IN A PORCINE ARTERIAL THROMBOSIS MODEL
    BELLINGER, DA
    NICHOLS, TC
    REDDICK, RL
    READ, MS
    KOCH, GG
    BRINKHOUS, KM
    GRIGGS, TR
    CIRCULATION, 1990, 82 (04) : 595 - 595