HETEROGENOUS PHENOTYPIC-EXPRESSION OF PLASMA AND PLATELET VONWILLEBRAND-FACTOR IN A PEDIGREE WITH VARIANT TYPE-IIC VONWILLEBRAND-DISEASE

被引:0
|
作者
LEDFORD, MR [1 ]
KENT, JW [1 ]
CIVANTOS, F [1 ]
机构
[1] UNIV MIAMI,SCH MED,DEPT PATHOL,MIAMI,FL 33152
关键词
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1124 / 1124
页数:1
相关论文
共 50 条
  • [21] THE BINDING OF VONWILLEBRAND-FACTOR TO COLLAGEN IS NORMAL IN TYPE-I BUT DEFECTIVE IN VARIANTS (TYPE IIA, IIB AND IIC) OF VONWILLEBRAND DISEASE
    NISHIKUBO, T
    TAKAHASHI, Y
    MORII, N
    FUKUI, H
    THROMBOSIS AND HAEMOSTASIS, 1991, 65 (06) : 1128 - 1128
  • [22] SUBUNIT COMPOSITION OF PLASMA VONWILLEBRAND-FACTOR - CLEAVAGE IS PRESENT IN NORMAL INDIVIDUALS, INCREASED IN IIA-VONWILLEBRAND DISEASE AND IIB-VONWILLEBRAND DISEASE, BUT MINIMAL IN VARIANTS WITH ABERRANT STRUCTURE OF INDIVIDUAL OLIGOMERS (TYPE-IIC, TYPE-IID, TYPE-IIE)
    ZIMMERMAN, TS
    DENT, JA
    RUGGERI, ZM
    NANNINI, LH
    JOURNAL OF CLINICAL INVESTIGATION, 1986, 77 (03): : 947 - 951
  • [23] THE NORMANDY VARIANT OF VONWILLEBRAND DISEASE - CHARACTERIZATION OF A POINT MUTATION IN THE VONWILLEBRAND-FACTOR GENE
    GAUCHER, C
    JORIEUX, S
    MERCIER, B
    OUFKIR, D
    MAZURIER, C
    BLOOD, 1991, 77 (09) : 1937 - 1941
  • [24] UNEXPECTED RESULTS FOLLOWING TREATMENT OF PATIENTS WITH VONWILLEBRAND-DISEASE WITH A NEW HIGHLY PURIFIED VONWILLEBRAND-FACTOR CONCENTRATE
    ROTHSCHILD, C
    FRESSINAUD, E
    WOLF, M
    DREYFUS, M
    LAURIAN, Y
    PEYNAUDDEBAYLE, E
    GAZENGEL, C
    MEYER, D
    LARRIEU, MJ
    THROMBOSIS AND HAEMOSTASIS, 1991, 65 (06) : 1126 - 1126
  • [25] VONWILLEBRAND-FACTOR BINDS TO PLATELETS AND INDUCES AGGREGATION IN PLATELET-TYPE BUT NOT TYPE-IIB VONWILLEBRAND DISEASE
    MILLER, JL
    KUPINSKI, JM
    CASTELLA, A
    RUGGERI, ZM
    JOURNAL OF CLINICAL INVESTIGATION, 1983, 72 (05): : 1532 - 1542
  • [26] EXPRESSION OF VONWILLEBRAND-FACTOR IN PLASMA AND PLATELETS OF CATS
    WATERS, DC
    EATON, AH
    STEIDLEY, KR
    MCCARROLL, DR
    AMERICAN JOURNAL OF VETERINARY RESEARCH, 1989, 50 (02) : 201 - 204
  • [27] EXPRESSION OF VONWILLEBRAND-FACTOR BY ENDOTHELIAL-CELLS FROM A PATIENT WITH TYPE IIA VONWILLEBRAND DISEASE
    LEVENE, RB
    BOOYSE, FM
    CHEDIAK, J
    ZIMMERMAN, TS
    LIVINGSTON, DM
    LYNCH, DC
    CIRCULATION, 1986, 74 (04) : 407 - 407
  • [28] ROLE FOR PLATELET VONWILLEBRAND-FACTOR IN SUPPORTING PLATELET-VESSEL WALL INTERACTIONS IN VONWILLEBRAND DISEASE
    CASTILLO, R
    ESCOLAR, G
    MONTEAGUDO, J
    ORDINAS, A
    GARRIDO, M
    MOIA, M
    FEDERICI, AB
    MANNUCCI, PM
    AMERICAN JOURNAL OF HEMATOLOGY, 1989, 31 (03) : 153 - 158
  • [29] PLATELET - VONWILLEBRAND-FACTOR INTERACTIONS IN TYPE-IIB VONWILLEBRANDS DISEASE
    HOLMBERG, L
    KRISTOFFERSSON, AC
    LAMME, S
    NILSSON, IM
    AWIDI, A
    SOLUM, NO
    SCANDINAVIAN JOURNAL OF HAEMATOLOGY, 1985, 35 (03): : 305 - 314
  • [30] PLASMA AND PLATELET VONWILLEBRAND-FACTOR DEFECTS IN UREMIA - REPLY
    GRALNICK, HR
    AMERICAN JOURNAL OF MEDICINE, 1989, 87 (04): : 490 - 490