GENERALIZED ACCUMULATION OF NEUTRAL GLYCOSPHINGOLIPIDS WITH GM2 GANGLIOSIDE ACCUMULATION IN BRAIN

被引:33
|
作者
KRIVIT, W
LEE, J
MOLLER, J
SNYDER, PD
SWEELEY, CC
SHARP, HL
WRIGHT, F
DESNICK, RJ
机构
来源
AMERICAN JOURNAL OF MEDICINE | 1972年 / 52卷 / 06期
关键词
D O I
10.1016/0002-9343(72)90082-4
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:763 / &
相关论文
共 50 条
  • [31] Structural basis for the enzymatic resistance of the GM2 ganglioside
    Li, YT
    Li, SC
    Ishida, H
    Kiso, M
    Raimondi, L
    Bernardi, A
    Sonnino, S
    RECOGNITION OF CARBOHYDRATES IN BIOLOGICAL SYSTEMS, PART B: SPECIFIC APPLICATIONS, 2003, 363 : 242 - 264
  • [32] INCORPORATION AND METABOLISM OF GANGLIOSIDE GM2 IN SKIN FIBROBLASTS FROM NORMAL AND GM2 GANGLIOSIDOSIS SUBJECTS
    SONDERFELD, S
    CONZELMANN, E
    SCHWARZMANN, G
    BURG, J
    HINRICHS, U
    SANDHOFF, K
    EUROPEAN JOURNAL OF BIOCHEMISTRY, 1985, 149 (02): : 247 - 255
  • [33] GM2 GANGLIOSIDE AND ECTOPIC DENDRITOGENESIS IN STORAGE DISEASES
    WALKLEY, SU
    SIEGEL, DA
    JOURNAL OF NEUROCHEMISTRY, 1994, 62 : S78 - S78
  • [34] GM2 ganglioside as a regulator of pyramidal neuron dendritogenesis
    Walkley, SU
    Siegel, DA
    Dobrenis, K
    Zervas, M
    SPHINGOLIPIDS AS SIGNALING MODULATORS IN THE NERVOUS SYSTEM, 1998, 845 : 188 - 199
  • [35] APPROACHES TO AUGMENTING THE IMMUNOGENICITY OF THE GANGLIOSIDE GM2 IN MICE
    LIVINGSTON, PO
    CALVES, MJ
    NATOLI, EJ
    PROCEEDINGS OF THE AMERICAN ASSOCIATION FOR CANCER RESEARCH, 1986, 27 : 364 - 364
  • [36] The expression and characterization of ganglioside GM2 in pancreatic cancer
    Sasaki, Norihiko
    Hirabayashi, Kenichi
    Michishita, Masaki
    Takahashi, Kimimasa
    Hasegawa, Fumio
    Gomi, Fujiya
    Itakura, Yoko
    Nakamura, Naoya
    Toyoda, Masashi
    Ishiwata, Toshiyuki
    CANCER SCIENCE, 2021, 112 : 384 - 384
  • [37] Ganglioside GM2 is substrate for a sialidase in MDCK cells
    Marchesini, S
    Benaglia, G
    Piccinotti, A
    Bresciani, R
    Preti, A
    FEBS LETTERS, 1998, 428 (1-2) : 115 - 117
  • [38] CHARACTERIZATION OF ANTI-SERUMS FOR GANGLIOSIDE GM2
    SCHWERER, B
    LASSMANN, H
    BERNHEIMER, H
    HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE, 1980, 361 (09): : 1343 - 1343
  • [39] Interaction of the GM2 activator protein with sulfated and sialylated glycosphingolipids
    Hepbildikler, ST
    Wendeler, M
    Sandhoff, R
    Sandhoff, K
    RECOGNITION OF CARBOHYDRATES IN BIOLOGICAL SYSTEMS, PART B: SPECIFIC APPLICATIONS, 2003, 363 : 207 - 222
  • [40] Synthetic studies on sialoglyconjugates .94. Synthesis of 6'-GM2, a regioisomer of ganglioside GM2, for studying the mechanism of action of GM2 activator
    Ishida, H
    Ito, Y
    Tanahashi, E
    Li, YT
    Kiso, M
    Hasegawa, A
    CARBOHYDRATE RESEARCH, 1997, 302 (3-4) : 223 - 227