LUNG SCINTIGRAPHY IN PULMONARY CAPILLARY HEMANGIOMATOSIS - A RARE DISORDER CAUSING PRIMARY PULMONARY-HYPERTENSION

被引:24
|
作者
RUSH, C
LANGLEBEN, D
SCHLESINGER, RD
STERN, J
WANG, NS
LAMOUREUX, E
机构
[1] SIR MORTIMER B DAVIS JEWISH HOSP, DEPT MED, DIV CARDIOL, MONTREAL H3T 1E2, QUEBEC, CANADA
[2] SIR MORTIMER B DAVIS JEWISH HOSP, DEPT RADIOL, DIV NUCL MED, MONTREAL H3T 1E2, QUEBEC, CANADA
[3] SIR MORTIMER B DAVIS JEWISH HOSP, DEPT PATHOL, MONTREAL H3T 1E2, QUEBEC, CANADA
[4] MCGILL UNIV, DEPT PATHOL, MONTREAL H3A 2T5, QUEBEC, CANADA
关键词
D O I
10.1097/00003072-199112000-00007
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
The authors report the results of lung scintigraphy in two patients with primary pulmonary hypertension caused by pulmonary capillary hemangiomatosis, a rare disorder resulting from the proliferation of histologically normal capillaries in the lung. Perfusion studies revealed a nonhomogeneous pattern with some focal defects, similar to that seen with some other histologic types of primary pulmonary hypertension. The mechanisms underlying this reperfusion pattern are unknown.
引用
收藏
页码:913 / 917
页数:5
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