DIRECT DEMONSTRATION OF BINDING OF A LYSOSOMAL ENZYME, ALPHA-L-IDURONIDASE, TO RECEPTORS ON CULTURED FIBROBLASTS

被引:128
|
作者
ROME, LH
WEISSMANN, B
NEUFELD, EF
机构
[1] UNIV ILLINOIS,COLL MED,DEPT BIOL CHEM,CHICAGO,IL 60612
[2] NIAMDD,GENET & BIOCHEM BRANCH,BETHESDA,MD 20014
关键词
D O I
10.1073/pnas.76.5.2331
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:2331 / 2334
页数:4
相关论文
共 50 条
  • [21] METHOD FOR ALPHA-L-IDURONIDASE ASSAY
    SINGH, J
    NIEBES, P
    DIFERRAN.N
    FEBS LETTERS, 1974, 45 (01): : 248 - 251
  • [22] MICROTEST FOR DETERMINATION OF ALPHA-L-IDURONIDASE IN PLASMA AND LEUKOCYTES AND ITS POTENTIAL FOR DIAGNOSING ALPHA-L-IDURONIDASE DEFICIENCY
    DENTANDT, WR
    SCHARPE, S
    GIESBERTS, M
    POORTHUIS, BJ
    LANCET, 1984, 1 (8380): : 794 - 794
  • [23] Crystal structure of human alpha-L-iduronidase
    Maita, Nobuo
    Taniguchi, Hisaaki
    Sakuraba, Hitoshi
    ACTA CRYSTALLOGRAPHICA A-FOUNDATION AND ADVANCES, 2011, 67 : C300 - C300
  • [24] HUMAN-PLASMA ALPHA-L-IDURONIDASE
    DENTANDT, WR
    ARCHIVES INTERNATIONALES DE PHYSIOLOGIE DE BIOCHIMIE ET DE BIOPHYSIQUE, 1987, 95 (05): : B190 - B190
  • [25] HURLERS SYNDROME, AN ALPHA-L-IDURONIDASE DEFICIENCY
    MATALON, R
    DORFMAN, A
    BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1972, 47 (04) : 959 - &
  • [26] Alpha-L-iduronidase pseudodeficiency: a case series
    Cagle, Stephanie
    Schroer, Richard
    Pollard, Laura
    Wood, Tim
    Coffee, Bradford
    MOLECULAR GENETICS AND METABOLISM, 2014, 111 (02) : S29 - S29
  • [27] PHENOTYPIC VARIATION IN ALPHA-L-IDURONIDASE DEFICIENCY
    LEISTI, J
    RIMOIN, DL
    KABACK, MM
    HOLLISTER, DW
    DENTANDT, W
    NEUFELD, E
    MATALON, R
    PHILIPPART, M
    LANCET, 1975, 1 (7920): : 1344 - 1344
  • [28] STRUCTURE AND MAPPING OF THE ALPHA-L-IDURONIDASE GENE
    SCOTT, HS
    HOPWOOD, JJ
    MORRIS, CP
    AMERICAN JOURNAL OF HUMAN GENETICS, 1991, 49 (04) : 414 - 414
  • [29] NEW SUBSTRATES FOR ASSAY OF ALPHA-L-IDURONIDASE
    THOMPSON, JN
    AMERICAN JOURNAL OF HUMAN GENETICS, 1977, 29 (06) : A107 - A107
  • [30] THE CLINICAL SPECTRUM OF ALPHA-L-IDURONIDASE DEFICIENCY
    ROUBICEK, M
    GEHLER, J
    SPRANGER, J
    AMERICAN JOURNAL OF MEDICAL GENETICS, 1985, 20 (03): : 471 - 481