EFFECTS OF DIMETHYLSULFOXIDE ON SPHINGOMYELINASE ACTIVITIES IN NORMAL AND NIEMANN-PICK TYPE-A, TYPE-B AND TYPE-C FIBROBLASTS

被引:0
|
作者
SATO, M
YOSHIDA, Y
SAKURAGAWA, N
ARIMA, M
机构
[1] NATL CTR HOSP MENTAL NERVOUS & MUSCULAR DISORDERS, NATL CTR NEUROL & PSYCHIAT, DIV CHILD NEUROL, KODAIRA, TOKYO 187, JAPAN
[2] NATL INST NEUROL SCI, DIV MENTAL RETARDAT & BIRTH DEFECT RES, TOKYO, JAPAN
关键词
D O I
暂无
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:59 / 65
页数:7
相关论文
共 50 条
  • [41] HYPERLIPIDEMIA AS A COMPLICATION OF NIEMANN-PICK TYPE-B DISEASE
    FILLINGKATZ, M
    FINK, JK
    OLIVER, KL
    KANESKI, C
    MERRICK, HF
    ARGOFF, CE
    BARTON, N
    BRADY, RO
    GREGG, RE
    CLINICAL PEDIATRICS, 1990, 29 (11) : 670 - 673
  • [42] OCULAR INVOLVEMENT IN NIEMANN-PICK DISEASE, TYPE-B
    LIPSON, M
    ODONNELL, J
    CALLAHAN, JW
    WENGER, D
    PACKMAN, S
    PEDIATRIC RESEARCH, 1985, 19 (04) : A315 - A315
  • [43] BIOSYNTHESIS OF SPHINGOMYELINASE IN NORMAL AND NIEMANN-PICK FIBROBLASTS
    JOBB, EA
    CALLAHAN, JW
    BIOCHEMISTRY AND CELL BIOLOGY-BIOCHIMIE ET BIOLOGIE CELLULAIRE, 1989, 67 (11-12): : 801 - 807
  • [44] Niemann-Pick; Type C
    Patterson, MC
    Pentchev, PG
    NEUROLOGY, 1996, 46 (06) : 1785 - 1786
  • [45] SPHINGOMYELINASE DEFICIENCY (NIEMANN-PICK) TYPE-A - NEW VARIANT WITH AN UNUSUALLY PROTRACTED COURSE
    ELLEDER, M
    CIHULA, J
    VANIER, MT
    SBORNIK LEKARSKY, 1988, 90 (01): : 21 - 25
  • [46] Dynamics of lysosomal cholesterol in Niemann-Pick type C and normal human fibroblasts
    Lange, Y
    Ye, J
    Rigney, M
    Steck, TL
    JOURNAL OF LIPID RESEARCH, 2002, 43 (02) : 198 - 204
  • [47] PRENATAL-DIAGNOSIS OF NIEMANN-PICK DISEASE TYPE-C
    DEWINTER, JM
    JANSE, HC
    VANDIGGELEN, OP
    LOS, FJ
    BEEMER, FA
    KLEIJER, WJ
    CLINICA CHIMICA ACTA, 1992, 208 (03) : 173 - 181
  • [48] CLINICAL ASPECTS OF NIEMANN-PICK TYPE-C DISEASE IN THE ADULT
    TURPIN, JC
    MASSON, M
    BAUMANN, N
    DEVELOPMENTAL NEUROSCIENCE, 1991, 13 (4-5) : 304 - 306
  • [49] INFANT WITH NIEMANN-PICK DISEASE TYPE-C AND EARLY CHOLOSTASIS
    BURY, F
    JAEKEN, J
    EGGERMONT, E
    LIBERT, J
    DENTANDT, W
    MARIEN, J
    DEVOS, R
    VANDAMME, B
    CORBEEL, L
    PEDIATRIE, 1979, 34 (04): : 351 - 357
  • [50] NIEMANN-PICK DISEASE TYPE-C - SKIN BIOPSIES IN PARENTS
    CEUTERICK, C
    MARTIN, JJ
    FOULARD, M
    NEUROPEDIATRICS, 1986, 17 (02) : 111 - 112