STUDIES ON TYPE-II GLYCOGENOSIS - EFFECTS OF CORTISONE DERIVATIVES ON ACID ALPHA-GLUCOSIDASE

被引:5
|
作者
BOURNE, EJ
CLARKE, K
PRIDHAM, JB
ROWE, JJM
机构
关键词
D O I
10.1042/bj1210663
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:663 / &
相关论文
共 50 条
  • [21] Adult glycogenosis type II (Pompe's disease): morphological abnormalities in muscle and skin biopsies compared with acid alpha-glucosidase activity
    Wierzba-Bobrowicz, Teresa
    Lewandowska, Eliza
    Lugowska, Agnieszka
    Rola, Rafal
    Stepien, Tomasz
    Ryglewicz, Danuta
    Pasennik, Elzbieta
    FOLIA NEUROPATHOLOGICA, 2007, 45 (04) : 179 - 186
  • [22] GLYCOGENOSIS TYPE-II (ACID MALTASE DEFICIENCY)
    REUSER, AJJ
    KROOS, MA
    HERMANS, MMP
    BIJVOET, AGA
    VERBEET, MP
    VANDIGGELEN, OP
    KLEIJER, WJ
    VANDERPLOEG, AT
    MUSCLE & NERVE, 1995, : S61 - S69
  • [23] TYPE-II GLYCOGENOSIS
    JORAM, A
    FESSARD, C
    TRON, P
    DEMENIBU.CH
    DAILLY, R
    SEMAINE DES HOPITAUX, 1974, 50 (07): : 489 - 495
  • [24] PREPARATION OF MONOCLONAL-ANTIBODIES AGAINST ACID ALPHA-D-GLUCOSIDASE FOR STUDY OF CHINESE GLYCOGENOSIS TYPE-II PATIENTS
    LIN, CY
    LEE, SY
    CHANG, ZN
    SU, SN
    HWANG, B
    HAN, SH
    HYBRIDOMA, 1992, 11 (04): : 493 - 505
  • [25] ACID ALPHA-GLUCOSIDASE DEFICIENCY IN CULTURED FIBROBLASTS WITH PHENOTYPE 2 OF ACID ALPHA-GLUCOSIDASE
    BERATIS, NG
    WILBUR, L
    SKLOWER, SL
    CLINICA CHIMICA ACTA, 1983, 134 (1-2) : 11 - 16
  • [26] INHIBITION OF BOVINE ALPHA-GLUCOSIDASE BY CASTANOSPERMUM-AUSTRALE AND ITS EFFECT ON THE BIOCHEMICAL-IDENTIFICATION OF HETEROZYGOTES FOR GENERALIZED GLYCOGENOSIS TYPE-II (POMPES DISEASE) IN CATTLE
    REICHMANN, KG
    TWIST, JO
    MCKENZIE, RA
    ROWAN, KJ
    AUSTRALIAN VETERINARY JOURNAL, 1987, 64 (09) : 274 - 276
  • [27] LEUKOCYTE ALPHA-1,4-GLUCOSIDASE AND ALPHA-1,6-GLUCOSIDASE ACTIVITIES TOWARDS OLIGOSACCHARIDES IN LATE ONSET GLYCOGENOSIS TYPE-II
    KURIYAMA, M
    HIWATARI, R
    OSAME, M
    IGATA, A
    TOHOKU JOURNAL OF EXPERIMENTAL MEDICINE, 1990, 161 (04): : 343 - 351
  • [28] LYSOSOMAL ALPHA-GLUCOSIDASE IN TYPE 2 GLYCOGENOSIS - ACTIVITY IN LEUKOCYTES AND CELL CULTURES IN RELATION TO GENOTYPE
    NITOWSKY, HM
    GRUNFELD, A
    JOURNAL OF LABORATORY AND CLINICAL MEDICINE, 1967, 69 (03): : 472 - +
  • [29] BIOCHEMICAL GENETICS OF THE LAPLAND DOG-MODEL OF GLYCOGEN-STORAGE DISEASE TYPE-II (ACID ALPHA-GLUCOSIDASE DEFICIENCY)
    WALVOORT, HC
    SLEE, RG
    SLUIS, KJ
    KOSTER, JF
    REUSER, AJJ
    AMERICAN JOURNAL OF MEDICAL GENETICS, 1984, 19 (03): : 589 - 598
  • [30] TYPE-II GLYCOGENOSIS IN ADULTS
    HUG, G
    SCHUBERT, WK
    SOUKUP, SW
    NEW ENGLAND JOURNAL OF MEDICINE, 1973, 288 (04): : 216 - 217