PROGRESSIVE UNILATERAL HYPERTROPHIC MYOPATHY - A CASE-STUDY

被引:3
|
作者
PIHKO, H
LEHTINEN, I
TIKKANEN, H
HARKONEN, M
RAPOLA, J
LAMMINEN, A
SAHLMAN, A
SOMER, H
机构
[1] TURKU CITY HOSP,CLIN NEUROPHYSIOL LAB,TURKU,FINLAND
[2] UNIV HELSINKI,DEPT OPT,SF-00100 HELSINKI 10,FINLAND
[3] UNIV HELSINKI,DEPT NEUROL,SF-00100 HELSINKI 10,FINLAND
[4] UNIV HELSINKI,DEPT SURG,SF-00100 HELSINKI 10,FINLAND
[5] UNIV HELSINKI,DEPT SURG RES,SF-00100 HELSINKI 10,FINLAND
[6] UNIV HELSINKI,DEPT CLIN CHEM,SF-00100 HELSINKI 10,FINLAND
[7] UNIV HELSINKI,DEPT CLIN NEUROL,SF-00100 HELSINKI 10,FINLAND
关键词
COMPLEX REPETITIVE DISCHARGES (CRD); FOCAL PROGRESSIVE MYOPATHY; MUSCLE HYPERTROPHY;
D O I
10.1002/mus.880160111
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 12-year-old girl had progressive unilateral muscle hypertrophy limited to the sole, tibialis anterior, and biceps femoris muscles. The affected muscles showed complex repetitive discharges by electromyography, necrosis and variation of fiber size upon histopathological examination, and increased metabolic activity in biochemical studies. The findings suggest a myopathic origin, but the actual cause remains unknown.
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页码:63 / 68
页数:6
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