The challenge of managing pulmonary arterial hypertension in adults with congenital heart disease

被引：12

作者：

Radke, Robert M. ^{[1
]}

Diller, Gerhard-Paul ^{[1
]}

Baumgartner, Helmut ^{[1
]}

机构：

[1] Univ Hosp Munster, Adult Congenital & Valvular Heart Dis Ctr, Dept Cardiol & Angiol, Munster, Germany

来源：

EXPERT REVIEW OF CARDIOVASCULAR THERAPY | 2013年 / 11卷 / 07期

关键词：

bosentan; congenital heart disease; disease-targeting therapies; Eisenmenger syndrome; endothelin receptor antagonists; phosphodiesterase-inhibitors; pulmonary arterial hypertension; shunt lesions; sildenafil;

D O I：

10.1586/14779072.2013.811966

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A significant number of adult patients with congenital heart disease suffer from pulmonary arterial hypertension leading to a markedly increased morbidity and mortality. Some defects may be eligible for operative or interventional repair in adulthood but careful selection of candidates is crucial. With the emergence of disease-targeting therapies, symptomatic improvement and stabilization have become possible while the impact on survival currently remains unclear.

引用

页码：919 / 931

页数：13

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