CHARACTERIZATION OF OLIGOSACCHARIDES AND GLYCOPEPTIDES EXCRETED IN URINE OF GM1-GANGLIOSIDOSIS PATIENTS

被引:14
|
作者
NGYINGKIN, NMK [1 ]
WOLFE, LS [1 ]
机构
[1] MCGILL UNIV,MONTREAL NEUROL INST,DONNER LAB EXPTL NEUROCHEM,MONTREAL H3A 2B4,QUEBEC,CANADA
关键词
D O I
10.1016/S0006-291X(75)80303-2
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:123 / 130
页数:8
相关论文
共 50 条
  • [21] GM1-GANGLIOSIDOSIS TYPE-II
    HOOFT, C
    VLIETINC.RF
    DACREMON.G
    KINT, JA
    EUROPEAN NEUROLOGY, 1970, 4 (01) : 1 - &
  • [22] Chemical chaperone therapy for GM1-gangliosidosis
    Suzuki, Y.
    CELLULAR AND MOLECULAR LIFE SCIENCES, 2008, 65 (03) : 351 - 353
  • [23] LIPID COMPOSITIONS IN THE BRAIN OF GM1-GANGLIOSIDOSIS
    KASAMA, T
    HARA, A
    TAKETOMI, T
    NEUROCHEMICAL RESEARCH, 1983, 8 (06) : 820 - 820
  • [24] Effects of cyclodextrins on GM1-gangliosides in fibroblasts from GM1-gangliosidosis patients
    Maeda, Yuki
    Motoyama, Keiichi
    Higashi, Taishi
    Horikoshi, Yuka
    Takeo, Toru
    Nakagata, Naomi
    Kurauchi, Yuki
    Katsuki, Hiroshi
    Ishitsuka, Yoichi
    Kondo, Yuki
    Irie, Tetsumi
    Furuya, Hirokazu
    Era, Takumi
    Arima, Hidetoshi
    JOURNAL OF PHARMACY AND PHARMACOLOGY, 2015, 67 (08) : 1133 - 1142
  • [25] STRUCTURES OF OLIGOSACCHARIDES AND GLYCOPEPTIDES IN URINE OF GM1 AND GM2 GANGLIOSIDOSES
    NGYINGKIN, NMK
    WOLFE, LS
    FEDERATION PROCEEDINGS, 1975, 34 (03) : 634 - 634
  • [26] OLIGOSACCHARIDE STORAGE IN BRAINS FROM PATIENTS WITH FUCOSIDOSIS, GM1-GANGLIOSIDOSIS AND GM2-GANGLIOSIDOSIS (SANDHOFFS DISEASE)
    TSAY, GC
    DAWSON, G
    JOURNAL OF NEUROCHEMISTRY, 1976, 27 (03) : 733 - 740
  • [27] STRUCTURE OF 7 OLIGOSACCHARIDES EXCRETED IN URINE OF A PATIENT WITH SANDHOFFS DISEASE (GM2 GANGLIOSIDOSIS-VARIANT O)
    STRECKER, G
    HERLANTPEERS, MC
    FOURNET, B
    MONTREUIL, J
    DORLAND, L
    HAVERKAMP, J
    VLIEGENTHART, JFG
    FARRIAUX, JP
    EUROPEAN JOURNAL OF BIOCHEMISTRY, 1977, 81 (01): : 165 - 171
  • [28] GM1-Gangliosidosis Type III Associated Parkinsonism
    Kaiyrzhanov, Rauan
    Guliyeva, Ulviyya
    Gulieva, Sughra
    Salayev, Kamran
    Mursalova, Aytan
    Allahyarova, Parvin
    Ferla, Matteo P.
    Houlden, Henry
    MOVEMENT DISORDERS CLINICAL PRACTICE, 2021, 8 : S21 - S23
  • [29] HEPATIC GLYCOSPHINGOLIPID ABNORMALITIES IN A PATIENT WITH GM1-GANGLIOSIDOSIS
    HARA, A
    TAKETOMI, T
    JOURNAL OF BIOCHEMISTRY, 1984, 96 (04): : 1051 - 1059
  • [30] RADIOGRAPHIC SKELETAL CHANGES IN JUVENILE GM1-GANGLIOSIDOSIS
    OWMAN, T
    SJOBLAD, S
    GOTHLIN, J
    FORTSCHRITTE AUF DEM GEBIETE DER RONTGENSTRAHLEN UND DER NUKLEARMEDIZIN, 1980, 132 (06): : 682 - 688