MAFFUCCIS-SYNDROME ASSOCIATED WITH INTRACRANIAL ENCHONDROMA AND ANEURYSM - CASE-REPORT

被引:35
|
作者
CHAKRABORTTY, S [1 ]
TAMAKI, N [1 ]
KONDOH, T [1 ]
KOJIMA, N [1 ]
KAMIKAWA, H [1 ]
MATSUMOTO, S [1 ]
机构
[1] KOBE UNIV, SCH MED,DEPT NEUROSURG,5-1 KUSUNOKI CHO,7 CHOME, CHUO KU, KOBE 650, JAPAN
来源
SURGICAL NEUROLOGY | 1991年 / 36卷 / 03期
关键词
GOITER; INTRACRANIAL ANEURYSM; INTRACRANIAL CHONDROMATOSIS; MAFFUCCIS SYNDROME;
D O I
10.1016/0090-3019(91)90116-Q
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Maffucci's syndrome is a rare, congenital mesodermal dysplasia combined with dyschondroplasia and hemangiomatosis. Enchondromatous involvement of the skull bones is rare in this syndrome. A rare case of Maffucci's syndrome associated with enchondroma at the skull base, left internal carotid artery aneurysm, and goiter is reported. Two other previously reported cases of Maffucci's syndrome with associated aneurysms and the present case suggest that Maffucci's syndrome may be associated with aneurysm.
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页码:216 / 220
页数:5
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