PULMONARY-HYPERTENSION ASSOCIATED WITH NONCIRRHOTIC PORTAL-HYPERTENSION IN SYSTEMIC LUPUS-ERYTHEMATOSUS

被引:16
|
作者
WOOLF, D
VOIGT, MD
JASKIEWICZ, K
KALLA, AA
机构
[1] UNIV CAPE TOWN OBSERV,RHEUMAT DIS UNIT,CAPE TOWN 7925,SOUTH AFRICA
[2] UNIV CAPE TOWN OBSERV,DEPT MED,CAPE TOWN 7925,SOUTH AFRICA
[3] UNIV CAPE TOWN OBSERV,MRC,UCT LIVER RES CTR,CAPE TOWN 7925,SOUTH AFRICA
关键词
D O I
10.1136/pgmj.70.819.41
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A case of non-cirrhotic portal hypertension in a patient with systemic lupus erythematosus, the first to our knowledge, is described. Severe pulmonary hypertension was associated with the portal hypertension and with markers of active auto-immunity. Pulmonary hypertension has not previously been associated with non-cirrhotic portal hypertension. The coexistence of vasculopathy of the portal and pulmonary vascular beds in this patient with active autoimmunity supports the postulate that portal-pulmonary hypertension may be immunologically mediated.
引用
收藏
页码:41 / 43
页数:3
相关论文
共 50 条
  • [21] PULMONARY-HYPERTENSION IN SYSTEMIC LUPUS-ERYTHEMATOSUS - A REPORT OF 4 CASES
    HODSON, P
    KLEMP, P
    MEYERS, OL
    [J]. CLINICAL AND EXPERIMENTAL RHEUMATOLOGY, 1983, 1 (03) : 241 - 245
  • [22] ABNORMAL PROSTANOID METABOLISM IN SYSTEMIC LUPUS-ERYTHEMATOSUS WITH PULMONARY-HYPERTENSION
    YOSHIDA, T
    KAMEDA, H
    AKIZUKI, M
    IKEDA, Y
    HOMMA, M
    ICHIKAWA, Y
    [J]. JOURNAL OF RHEUMATOLOGY, 1994, 21 (12) : 2393 - 2394
  • [23] PULMONARY-HYPERTENSION IN SYSTEMIC LUPUS-ERYTHEMATOSUS - A REPORT OF 3 CASES
    ASHERSON, RA
    HACKETT, D
    GHARAVI, AE
    HARRIS, EN
    KENNEDY, HG
    HUGHES, GRV
    [J]. JOURNAL OF RHEUMATOLOGY, 1986, 13 (02) : 416 - 420
  • [24] PULMONARY-HYPERTENSION IN SYSTEMIC LUPUS-ERYTHEMATOSUS - A REPORT OF AN AUTOPSIED CASE
    SATO, M
    OKAZAKI, H
    OKAMOTO, H
    OHTAKA, A
    SHIMIZU, H
    MINATO, N
    KANO, S
    [J]. INTERNAL MEDICINE, 1994, 33 (09) : 540 - 542
  • [25] PULMONARY-HYPERTENSION IN SYSTEMIC LUPUS-ERYTHEMATOSUS - CASE-REPORT
    CHAROENPAN, P
    SUKUMALCHANTRA, Y
    ISARANKULNAAYUTHYA, W
    [J]. JOURNAL OF THE MEDICAL ASSOCIATION OF THAILAND, 1977, 60 (12): : 670 - 675
  • [26] PULMONARY-HYPERTENSION IN SYSTEMIC LUPUS-ERYTHEMATOSUS - EFFECT OF VASODILATORS ON PULMONARY HEMODYNAMICS
    MAHOWALD, ML
    WEIR, EK
    RIDLEY, DJ
    MESSNER, RP
    [J]. JOURNAL OF RHEUMATOLOGY, 1985, 12 (04) : 773 - 777
  • [27] 2 CASES OF PULMONARY-HYPERTENSION WITH RAYNAUDS-PHENOMENON - PRIMARY PULMONARY-HYPERTENSION AND SYSTEMIC LUPUS-ERYTHEMATOSUS
    KANEMOTO, N
    GONDA, N
    KATSU, M
    FUKUDA, J
    [J]. JAPANESE HEART JOURNAL, 1975, 16 (03): : 354 - 360
  • [28] PULMONARY HYPERTENSION IN SYSTEMIC LUPUS-ERYTHEMATOSUS
    MACK, JW
    FRY, MB
    MCINTOSH, DA
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1973, 289 (03): : 157 - 158
  • [29] PULMONARY-HYPERTENSION WITH COEXISTING PORTAL-HYPERTENSION
    ROSSI, SO
    GILBERTBARNESS, E
    SAARI, T
    CORLISS, R
    [J]. PEDIATRIC PATHOLOGY, 1992, 12 (03): : 433 - 439
  • [30] PULMONARY-HYPERTENSION COMPLICATING PORTAL-HYPERTENSION
    LEBREC, D
    CAPRON, JP
    DHUMEAUX, D
    BENHAMOU, JP
    [J]. AMERICAN REVIEW OF RESPIRATORY DISEASE, 1979, 120 (04): : 849 - 856