PULMONARY-HYPERTENSION ASSOCIATED WITH NONCIRRHOTIC PORTAL-HYPERTENSION IN SYSTEMIC LUPUS-ERYTHEMATOSUS

被引:16
|
作者
WOOLF, D
VOIGT, MD
JASKIEWICZ, K
KALLA, AA
机构
[1] UNIV CAPE TOWN OBSERV,RHEUMAT DIS UNIT,CAPE TOWN 7925,SOUTH AFRICA
[2] UNIV CAPE TOWN OBSERV,DEPT MED,CAPE TOWN 7925,SOUTH AFRICA
[3] UNIV CAPE TOWN OBSERV,MRC,UCT LIVER RES CTR,CAPE TOWN 7925,SOUTH AFRICA
关键词
D O I
10.1136/pgmj.70.819.41
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A case of non-cirrhotic portal hypertension in a patient with systemic lupus erythematosus, the first to our knowledge, is described. Severe pulmonary hypertension was associated with the portal hypertension and with markers of active auto-immunity. Pulmonary hypertension has not previously been associated with non-cirrhotic portal hypertension. The coexistence of vasculopathy of the portal and pulmonary vascular beds in this patient with active autoimmunity supports the postulate that portal-pulmonary hypertension may be immunologically mediated.
引用
收藏
页码:41 / 43
页数:3
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