RELAPSING POLYCHONDRITIS AND RETROPERITONEAL FIBROSIS IN AN 8-YEAR-OLD BOY

被引:17
|
作者
BLAU, EB [1 ]
机构
[1] UNIV PITTSBURGH, SCH MED, DEPT PEDIAT, PITTSBURGH, PA 15213 USA
来源
关键词
D O I
10.1001/archpedi.1976.02120110111018
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
An 8 year old boy with symptoms of relapsing polychondritis for 5 yr developed retroperitoneal fibrosis and ureteral obstruction. In addition to involvement of the cartilage of his joints, ear and nose, there was significant arterial involvement. The patient had a very good response to adrenal corticosteroid therapy. After 1 yr of follow-up, he had a definite increase in joint mobility and normal renal function.
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页码:1149 / 1152
页数:4
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