IDIOPATHIC PULMONARY HILAR FIBROSIS - AN UNUSUAL CAUSE OF PULMONARY-HYPERTENSION

被引:12
|
作者
ESPINOSA, RE
EDWARDS, WD
ROSENOW, EC
SCHAFF, HV
机构
[1] MAYO CLIN ROCHESTER,DIV CARDIOVASC DIS & INTERNAL MED,ROCHESTER,MN
[2] MAYO CLIN ROCHESTER,DIV THORAC & CARDIOVASC SURG,ROCHESTER,MN
[3] MAYO CLIN ROCHESTER,DIV ANAT PATHOL,ROCHESTER,MN
[4] MAYO CLIN ROCHESTER,DIV THORAC DIS & INTERNAL MED,ROCHESTER,MN
关键词
D O I
10.1016/S0025-6196(12)60636-3
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A 37-year-old man with progressive exertional dyspnea had pulmonary hypertension associated with pulmonary arterial and venous obstruction. An autopsy revealed that the cause of death was idiopathic pulmonary hilar fibrosis, a variant of mediastinal fibrosis. Pulmonary hilar fibrosis can mimic thromboembolic pulmonary hypertension, pulmonary veno-occlusive disease, and pulmonary venous hypertension.
引用
收藏
页码:778 / 782
页数:5
相关论文
共 50 条
  • [31] Pulmonary hypertension in idiopathic pulmonary fibrosis: Utility of HRCT
    Mazzei, Maria Antonietta
    Bettini, Gloria
    Castria, Donatella
    Refini, Rosa Metella
    Bennet, David
    Kacerja, Esmeralda
    De Negri, Ferdinando
    Volterrani, Luca
    Rottoli, Paola
    EUROPEAN RESPIRATORY JOURNAL, 2014, 44
  • [32] Pulmonary Hypertension in Idiopathic Pulmonary Fibrosis: A New Phenotype?
    Redondo, Margarida
    Costa, Diogo
    Melo, Natalia
    Mota, Patricia
    Morais, Antonio
    CHEST, 2014, 145 (03)
  • [33] Precocious detection of pulmonary hypertension in idiopathic pulmonary fibrosis
    Castria, Donatella
    Refini, Rosa Metella
    Mezzasalma, Fabrizio
    Di Sipio, Pasquale
    Bargagli, Elena
    Filippi, Rita
    Pierli, Carlo
    Rottoli, Paola
    EUROPEAN RESPIRATORY JOURNAL, 2012, 40
  • [34] Pulmonary Hypertension as a Prognostic Factor in Idiopathic Pulmonary Fibrosis
    Aggarwal, Deepak
    Aggarwal, Phiza
    RESPIRATION, 2013, 85 (06) : 521 - 521
  • [35] Bosentan for pulmonary hypertension secondary to idiopathic pulmonary fibrosis
    Onda, Naomi
    Tanaka, Yosuke
    Hino, Mitsunori
    Gemma, Akihiko
    RESPIRATORY MEDICINE CASE REPORTS, 2015, 14 : 19 - 23
  • [36] IDIOPATHIC PULMONARY-HYPERTENSION - THERAPEUTIC OPPORTUNITIES AND PITFALLS
    MOSER, KM
    JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1982, 247 (22): : 3119 - 3119
  • [37] OUTCOMES IN PATIENTS WITH IDIOPATHIC PULMONARY FIBROSIS AND PULMONARY HYPERTENSION
    Collins, Ashley
    King, Christopher
    Shlobin, Oksana
    Nathan, Steven
    CHEST, 2020, 158 (04) : 1071A - 1072A
  • [38] Idiopathic pulmonary fibrosis and pulmonary hypertension - Connecting the dots
    Nathan, Steven D.
    Noble, Paul W.
    Tuder, Rubin M.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2007, 175 (09) : 875 - 880
  • [39] Pulmonary Hypertension and Idiopathic Pulmonary Fibrosis: A Dastardly Duo
    Smith, J. Shaun
    Gorbett, Daniel
    Mueller, Julianne
    Perez, Rafael
    Daniels, Curt J.
    AMERICAN JOURNAL OF THE MEDICAL SCIENCES, 2013, 346 (03): : 221 - 225
  • [40] THE NATURAL-HISTORY OF IDIOPATHIC PULMONARY-HYPERTENSION
    FUSTER, V
    GIULIANI, ER
    BRANDENBURG, RO
    WEIDMAN, WH
    EDWARDS, WD
    AMERICAN JOURNAL OF CARDIOLOGY, 1981, 47 (02): : 422 - 422