IDIOPATHIC PULMONARY HILAR FIBROSIS - AN UNUSUAL CAUSE OF PULMONARY-HYPERTENSION

被引:12
|
作者
ESPINOSA, RE
EDWARDS, WD
ROSENOW, EC
SCHAFF, HV
机构
[1] MAYO CLIN ROCHESTER,DIV CARDIOVASC DIS & INTERNAL MED,ROCHESTER,MN
[2] MAYO CLIN ROCHESTER,DIV THORAC & CARDIOVASC SURG,ROCHESTER,MN
[3] MAYO CLIN ROCHESTER,DIV ANAT PATHOL,ROCHESTER,MN
[4] MAYO CLIN ROCHESTER,DIV THORAC DIS & INTERNAL MED,ROCHESTER,MN
关键词
D O I
10.1016/S0025-6196(12)60636-3
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A 37-year-old man with progressive exertional dyspnea had pulmonary hypertension associated with pulmonary arterial and venous obstruction. An autopsy revealed that the cause of death was idiopathic pulmonary hilar fibrosis, a variant of mediastinal fibrosis. Pulmonary hilar fibrosis can mimic thromboembolic pulmonary hypertension, pulmonary veno-occlusive disease, and pulmonary venous hypertension.
引用
收藏
页码:778 / 782
页数:5
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