POEMS SYNDROME - FOLLOW-UP-STUDY OF A CASE

被引:19
|
作者
CRISCI, C
BARBIERI, F
PARENTE, D
PAPPONE, N
CARUSO, G
机构
[1] OSPED SACRO CUORE GESU, BENEVENTO, ITALY
[2] NAPLES UNIV, SCH MED 2, DEPT CLIN NEUROPHYSIOL, I-80125 NAPLES, ITALY
[3] NAPLES UNIV, SCH MED 2, DEPT NEUROL, I-80125 NAPLES, ITALY
关键词
POEMS; CIDP; POLYNEUROPATHY; CYCLOPHOSPHAMIDE; NERVE CONDUCTION VELOCITY;
D O I
10.1016/0303-8467(92)90122-J
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report here the case of a 20-year-old man with POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, M proteins, skin changes). This rare syndrome followed a 3-year history of a syndrome that mimicks a chronic inflammatory demyelinating polyneuropathy (CIDP). Treatment with cyclophosphamide induced regression of the syndrome and improved peripheral nerve conduction.
引用
收藏
页码:65 / 68
页数:4
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