SNEDDON SYNDROME - GENERALIZED LIVEDO-RETICULARIS AND CEREBROVASCULAR-DISEASE - IMPORTANCE OF HEMOSTATIC SCREENING

被引:13
|
作者
DEVOS, J
BULCKE, J
DEGREEF, H
MICHIELSEN, B
机构
[1] CATHOLIC UNIV LEUVEN,DEPT NEUROL,B-3000 LOUVAIN,BELGIUM
[2] CATHOLIC UNIV LEUVEN,DEPT DERMATOL,B-3000 LOUVAIN,BELGIUM
关键词
SNEDDON SYNDROME; HEMOSTATIC EXAMINATION; ACETYLSALICYLIC ACID;
D O I
10.1159/000247474
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
We report two cases of Sneedon's syndrome. Both cases had widespread livedo reticularis with repeated cerebrovascular accidents without persistent neurological deficit. In one case, hemostatic examination revealed an imbalance of plasminogen activator-inhibitor values, possibly related to the thrombogenic propensity of the syndrome. Treatment with acetylsalicylic acid led to normalization of hemostatic parameters and resulted in a symptom-free period of more than 10 months. The importance of hemostatic screening in patients with Sneddon's syndrome is discussed.
引用
收藏
页码:296 / 299
页数:4
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