Only one report of congenital biliary cysts has been described so far from India, and that was in children. We present our experience with 22 adult Indian patients with this condition. The main presenting symptoms were abdominal pain, icterus, and fever, and the classical triad of jaundice, pain, and abdominal mass was seen in only one patient. The mean age of presentation was 25.5 +/- 10.1 yr, and females predominated (82%). Type Ia cysts (fusiform choledochal cyst) were the commonest. Intrahepatic cysts were seen in four patients; three of these were associated with extrahepatic biliary ductal cysts (type IVa). Internal drainage procedures performed elsewhere in six patients were followed by recurrent cholangitis, necessitating excision of the cyst. Hence, the preferred operation for congenital biliary cysts is cyst excision and hepaticojejunostomy.
机构:Niigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Ohashi, Taku
Wakai, Toshifumi
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Niigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, JapanNiigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Wakai, Toshifumi
Kubota, Masayuki
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Niigata Univ, Grad Sch Med & Dent Sci, Div Pediat Surg, Niigata 9518510, JapanNiigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Kubota, Masayuki
Matsuda, Yasunobu
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Niigata Univ, Grad Sch Med & Dent Sci, Div Gastroenterol & Hepatol, Niigata 9518510, JapanNiigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Matsuda, Yasunobu
Arai, Yuhki
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Niigata Univ, Grad Sch Med & Dent Sci, Div Pediat Surg, Niigata 9518510, JapanNiigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Arai, Yuhki
Ohyama, Toshiyuki
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Niigata Univ, Grad Sch Med & Dent Sci, Div Pediat Surg, Niigata 9518510, JapanNiigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Ohyama, Toshiyuki
Nakaya, Kengo
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Niigata Univ, Grad Sch Med & Dent Sci, Div Pediat Surg, Niigata 9518510, JapanNiigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Nakaya, Kengo
Okuyama, Naoki
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Niigata Univ, Grad Sch Med & Dent Sci, Div Pediat Surg, Niigata 9518510, JapanNiigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Okuyama, Naoki
Sakata, Jun
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机构:Niigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Sakata, Jun
Shirai, Yoshio
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机构:Niigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
Shirai, Yoshio
Ajioka, Yoichi
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Niigata Univ, Grad Sch Med & Dent Sci, Div Mol & Diagnost Pathol, Niigata 9518510, JapanNiigata Univ, Grad Sch Med & Dent Sci, Div Digest & Gen Surg, Chuo Ku, Niigata 9518510, Japan
LIU Yingbin WANG Jianwei Khagendra Raj Devkota JI Zhenling LI Jiangtao WANG Xuan MA Xiaoming CAI Weilong KONG Ying CAO Liping PENG Shuyou Department of SurgeryLiu YBLi JTWang XAMa XMCai WLKong YCao LP and Peng SYDepartment of Oncological Surgery Wang JW and Devkota KRSecond Affiliated HospitalSchool of MedicineZhejiang UniversityHangzhou ChinaDepartment of SurgeryAffiliated Puji Hospital of Yangzhou UniversityTaizhou China JI ZL
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LIU Yingbin WANG Jianwei Khagendra Raj Devkota JI Zhenling LI Jiangtao WANG Xuan MA Xiaoming CAI Weilong KONG Ying CAO Liping PENG Shuyou Department of SurgeryLiu YBLi JTWang XAMa XMCai WLKong YCao LP and Peng SYDepartment of Oncological Surgery Wang JW and Devkota KRSecond Affiliated HospitalSchool of MedicineZhejiang UniversityHangzhou ChinaDepartment of SurgeryAffiliated Puji Hospital of Yangzhou UniversityTaizhou China JI ZL
LIU Ying-bin WANG Jian-wei Khagendra Raj Devkota JI Zhen-ling LI Jiang-tao WANG Xu-an MA Xiao-ming CAI Wei-long KONG Ying CAO Li-ping PENG Shu-you Department of Surgery
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LIU Ying-bin WANG Jian-wei Khagendra Raj Devkota JI Zhen-ling LI Jiang-tao WANG Xu-an MA Xiao-ming CAI Wei-long KONG Ying CAO Li-ping PENG Shu-you Department of Surgery
机构:
HBT Med Coll & Dr RN Cooper Municipal Gen Hosp, Dept Gen Surg, Mumbai, IndiaHBT Med Coll & Dr RN Cooper Municipal Gen Hosp, Dept Gen Surg, Mumbai, India
Ranvir, Deepak
Khalife, Asma
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Topiwala Natl Med Coll & BYL Nair Charitable Hosp, Dept Gen Surg, Mumbai, IndiaHBT Med Coll & Dr RN Cooper Municipal Gen Hosp, Dept Gen Surg, Mumbai, India
Khalife, Asma
Mahey, Rajeshkumar C.
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Topiwala Natl Med Coll & BYL Nair Charitable Hosp, Dept Gen Surg, Mumbai, IndiaHBT Med Coll & Dr RN Cooper Municipal Gen Hosp, Dept Gen Surg, Mumbai, India
Mahey, Rajeshkumar C.
Telang, Bhushan
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Govt Med Coll & Hosp, Dept Surg Oncol, Aurangabad, IndiaHBT Med Coll & Dr RN Cooper Municipal Gen Hosp, Dept Gen Surg, Mumbai, India
Telang, Bhushan
Soni, Gagan
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All India Inst Med Sci, Dept Surg, New Delhi, IndiaHBT Med Coll & Dr RN Cooper Municipal Gen Hosp, Dept Gen Surg, Mumbai, India
Soni, Gagan
Kothari, Abhi H.
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Topiwala Natl Med Coll & BYL Nair Charitable Hosp, Dept Gen Surg, Mumbai, IndiaHBT Med Coll & Dr RN Cooper Municipal Gen Hosp, Dept Gen Surg, Mumbai, India
Kothari, Abhi H.
Joshi, Rajeev
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Topiwala Natl Med Coll & BYL Nair Charitable Hosp, Dept Gen Surg, Mumbai, India
KJ Somaiya Med Coll & Res Ctr, Dept Gen Surg, Mumbai, IndiaHBT Med Coll & Dr RN Cooper Municipal Gen Hosp, Dept Gen Surg, Mumbai, India
机构:
China Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R ChinaChina Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R China
Liu, Yuan
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Yao, Xu
Li, Shuqiang
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China Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R ChinaChina Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R China
Li, Shuqiang
Liu, Wenhan
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China Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R ChinaChina Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R China
Liu, Wenhan
Liu, Lei
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China Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R ChinaChina Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R China
Liu, Lei
Liu, Jingang
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China Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R ChinaChina Med Univ, Shengjing Hosp, Dept Gen Surg, Shenyang 110004, Peoples R China