FATTY-ACID OXIDATION IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH INHERITED DISORDERS OF FATTY-ACID METABOLISM - STUDIES ON THE SPECIFICITY OF ACYL-COA DEHYDROGENASES

被引：3
|
作者：
CHALMERS, RA [1 ]
ENGLISH, N [1 ]
机构：
[1] MRC,CLIN RES CTR,HARROW HA1 3UJ,MIDDX,ENGLAND
来源：
BIOCHEMICAL SOCIETY TRANSACTIONS | 1987年 / 15卷 / 03期
关键词：
D O I：
10.1042/bst0150489
中图分类号：
Q5 [生物化学]; Q7 [分子生物学];
学科分类号：
071010 ; 081704 ;
摘要：
引用
下载
收藏
页码：489 / 489
页数：1
相关论文
共 50 条
  • [21] STUDIES OF FATTY ACID OXIDATION .3. EFFECTS OF ACYL-COA COMPLEXES ON FATTY ACID OXIDATION
    AVIGAN, J
    QUASTEL, JH
    SCHOLEFIELD, PG
    BIOCHEMICAL JOURNAL, 1955, 60 (1-4) : 329 - 334
  • [22] ACYL-COA MAY BE A NEGLECTED PRODUCT IN STUDIES OF FATTY-ACID SYNTHESIS BY ISOLATED-CHLOROPLASTS
    ROUGHAN, PG
    SLACK, CR
    FEBS LETTERS, 1981, 135 (01) : 182 - 186
  • [23] INHERITED DEFECTS OF MITOCHONDRIAL FATTY-ACID OXIDATION
    TURNBULL, DM
    SHEPHERD, IM
    AYNSLEYGREEN, A
    BIOCHEMICAL SOCIETY TRANSACTIONS, 1988, 16 (03) : 424 - 427
  • [24] Mitochondrial Fatty-Acid Oxidation Disorders
    Kompare, Michelle
    Rizzo, William B.
    SEMINARS IN PEDIATRIC NEUROLOGY, 2008, 15 (03) : 140 - 149
  • [25] DIAGNOSING DISORDERS OF FATTY-ACID OXIDATION
    NYHAN, WL
    CLINICAL CHEMISTRY, 1995, 41 (01) : 10 - 11
  • [26] HYPERURICEMIA IN DISORDERS OF FATTY-ACID OXIDATION
    COLE, DEC
    CLARKE, LA
    MCPHEE, MD
    STMARIE, M
    CLINICAL CHEMISTRY, 1988, 34 (04) : 795 - 796
  • [27] Identification of fatty acid oxidation disorder patients with lowered acyl-CoA thioesterase activity in human skin fibroblasts
    Hunt, MC
    Ruiter, J
    Mooyer, P
    van Roermond, CWT
    Ofman, R
    Ijlst, L
    Wanders, RJA
    EUROPEAN JOURNAL OF CLINICAL INVESTIGATION, 2005, 35 (01) : 38 - 46
  • [28] EFFECT OF FATTY-ACIDS AND THEIR ACYL-COA ESTERS ON PROTEIN-KINASE-C ACTIVITY IN FIBROBLASTS - POSSIBLE IMPLICATIONS IN FATTY-ACID OXIDATION DEFECTS
    NESHER, M
    BONEH, A
    BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH, 1994, 1221 (01): : 66 - 72
  • [29] EXCESS C26 FATTY-ACID IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH ADRENOLEUKODYSTROPHY
    MOSER, HW
    KAWAMURA, N
    KISHIMOTO, Y
    SCHAUMBURG, H
    SUZUKI, K
    MURPHY, J
    ANNALS OF NEUROLOGY, 1978, 4 (02) : 170 - 170
  • [30] ESSENTIAL FATTY-ACID METABOLISM IN CULTURED ASTROBLASTS
    ROBERT, J
    REBEL, G
    MANDEL, P
    BIOCHIMIE, 1977, 59 (04) : 417 - 423
12345