Polyunsaturated long-chain fatty acids in hyperphenylalaninemias

被引：0
|
作者：
Guillen-Lopez, Sara [1 ]
Rodriguez-Schmidt, Romina [2 ]
Vela-Amieva, Marcela [1 ]
机构：
[1] Inst Nacl Pediat, Lab Errores Innatos Metab & Tamiz, Mexico City, DF, Mexico
[2] Inst Nacl Pediat, Licenciada Nutr & Ciencia Alimentos, Mexico City, DF, Mexico
来源：
ACTA PEDIATRICA DE MEXICO | 2012年 / 33卷 / 06期
关键词：
Hyperphenylalaninemia; long chain fatty acids; docosahexaenoic acid;
D O I：
暂无
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
Patients with hyperphenylalaninemia (HFA) must follow a restricted protein diet, which deprives them of natural dietary sources of polyunsaturated fatty acids (LC-PUFA) that lead to neurological deficits, not related to high phenylalanine blood levels. There is strong evidence of the benefits of docosahexaenoic acid (DHA) supplement, a long chain polyunsaturated fatty acid (LC-PUFA) that has several essential roles in the brain and in the retina. More studies are required to determine the DHA dosage and its sources at different stages of life in this HFA patients.
引用
收藏
页码：335 / 339
页数：5
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