INCORPORATION AND DEGRADATION OF GM1 GANGLIOSIDE AND ASIALOGM1 GANGLIOSIDE IN CULTURED FIBROBLASTS FROM NORMAL INDIVIDUALS AND PATIENTS WITH BETA-GALACTOSIDASE DEFICIENCY

被引：0
|
作者：
KOBAYASHI, T
SHINNOH, N
KUROIWA, Y
机构：
来源：
BIOCHIMICA ET BIOPHYSICA ACTA | 1986年 / 875卷 / 01期
关键词：
D O I：
暂无
中图分类号：
Q5 [生物化学]; Q7 [分子生物学];
学科分类号：
071010 ; 081704 ;
摘要：
引用
收藏
页码：115 / 121
页数：7
相关论文
共 50 条
  • [41] A FLUOROMETRIC MICROASSAY PROCEDURE FOR MONITORING THE ENZYMATIC-ACTIVITY OF GM1-GANGLIOSIDE BETA-GALACTOSIDASE BY USE OF HIGH-PERFORMANCE LIQUID-CHROMATOGRAPHY
    KIUCHI, K
    MUTOH, T
    NAOI, M
    ANALYTICAL BIOCHEMISTRY, 1984, 140 (01) : 146 - 151
  • [42] Ganglioside GM1 Deficiency in Effector T Cells From NOD Mice Induces Resistance to Regulatory T-Cell Suppression
    Wu, Gusheng
    Lu, Zi-Hua
    Gabius, Hans-Joachim
    Ledeen, Robert W.
    Bleich, David
    DIABETES, 2011, 60 (09) : 2341 - 2349
  • [43] GM1 GANGLIOSIDE PARTIALLY RESCUES CULTURED DOPAMINERGIC-NEURONS FROM MPP+-INDUCED DAMAGE - DEPENDENCE ON INITIAL DAMAGE AND TIME OF TREATMENT
    STULL, ND
    SCHNEIDER, JS
    IACOVITTI, L
    BRAIN RESEARCH, 1994, 640 (1-2) : 308 - 315
  • [44] T cells from patients with Guillain-Barre syndrome produce interferon-gamma in response to stimulation with the ganglioside GM1
    McCombe, P. A.
    Csurhes, P. A.
    JOURNAL OF CLINICAL NEUROSCIENCE, 2010, 17 (04) : 537 - 538
  • [45] METABOLISM OF EXOGENOUS GANGLIOSIDE GM1 IN CULTURED CEREBELLAR GRANULE CELLS - THE FATTY-ACID AND SPHINGOSINE MOIETIES FORMED DURING DEGRADATION ARE RE-USED FOR LIPID BIOSYNTHESIS
    RIBONI, L
    BASSI, R
    CONTI, M
    TETTAMANTI, G
    FEBS LETTERS, 1993, 322 (03) : 257 - 260
  • [46] Transient high-level expression of ss-galactosidase after transfection of fibroblasts from GM1 gangliosidosis patients with plasmid DNA
    Balestrin, R. C.
    Baldo, G.
    Vieira, M. B.
    Sano, R.
    Coelho, J. C.
    Giugliani, R.
    Matte, U.
    BRAZILIAN JOURNAL OF MEDICAL AND BIOLOGICAL RESEARCH, 2008, 41 (04) : 283 - 288
  • [47] ACTIVATOR PROTEIN REQUIRED FOR THE ENZYMATIC-HYDROLYSIS OF CEREBROSIDE SULFATE - DEFICIENCY IN URINE OF PATIENTS AFFECTED WITH CEREBROSIDE SULFATASE ACTIVATOR DEFICIENCY AND IDENTITY WITH ACTIVATORS FOR THE ENZYMATIC-HYDROLYSIS OF GM1 GANGLIOSIDE AND GLOBOTRIAOSYLCERAMIDE
    LI, SC
    KIHARA, H
    SERIZAWA, S
    LI, YT
    FLUHARTY, AL
    MAYES, JS
    SHAPIRO, LJ
    JOURNAL OF BIOLOGICAL CHEMISTRY, 1985, 260 (03) : 1867 - 1871
  • [48] Identification of GM1-Ganglioside Secondary Accumulation in Fibroblasts from Neuropathic Gaucher Patients and Effect of a Trivalent Trihydroxypiperidine Iminosugar Compound on Its Storage Reduction
    Ceni, Costanza
    Clemente, Francesca
    Mangiavacchi, Francesca
    Matassini, Camilla
    Tonin, Rodolfo
    Caciotti, Anna
    Feo, Federica
    Coviello, Domenico
    Morrone, Amelia
    Cardona, Francesca
    Calamai, Martino
    MOLECULES, 2024, 29 (02):
  • [49] Molecular form and subcellular distribution of acid beta-galactosidase in fibroblasts from patients with G(M1) gangliosidosis, Morquio B disease and galactosialidosis
    Takiyama, N
    Itoh, K
    Shimmoto, M
    Nishimoto, J
    Inui, K
    Sakuraba, H
    Suzuki, Y
    BRAIN & DEVELOPMENT, 1997, 19 (02): : 126 - 130
  • [50] GALACTOSYLCERAMIDE-LOADING AND LACTOSYLCERAMIDE-LOADING STUDIES IN CULTURED FIBROBLASTS FROM NORMAL INDIVIDUALS AND PATIENTS WITH GLOBOID-CELL LEUKODYSTROPHY (KRABBES DISEASE) AND GM1-GANGLIOSIDOSIS
    KOBAYASHI, T
    SHINNOH, N
    GOTO, I
    KUROIWA, Y
    OKAWAUCHI, M
    SUGIHARA, G
    TANAKA, M
    BIOCHIMICA ET BIOPHYSICA ACTA, 1985, 835 (03) : 456 - 464
12345