The prune-belly syndrome: Current insights

被引:28
|
作者
Sutherland, RS [1 ]
Mevorach, RA [1 ]
Kogan, BA [1 ]
机构
[1] UNIV CALIF SAN FRANCISCO,SCH MED,DEPT UROL,SAN FRANCISCO,CA 94143
关键词
prune-belly syndrome;
D O I
10.1007/BF00868740
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
The prune-belly syndrome comprises a constellation of well-established physical findings, yet the cause and management remain controversial. This review focuses on the current understanding of its pathogenesis and characterizes the fetal and neonatal diagnosis and management. Other associated anomalies are discussed to understand better the factors affecting treatment and prognosis as these patients grow into childhood and beyond.
引用
收藏
页码:770 / 778
页数:9
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