SYNTHESIS OF AN ALTERED TYPE-III PROCOLLAGEN IN A PATIENT WITH TYPE-IV EHLERS-DANLOS SYNDROME - A STRUCTURAL-CHANGE IN THE ALPHA-1(III) CHAIN WHICH MAKES THE PROTEIN MORE SUSCEPTIBLE TO PROTEINASES

被引:0
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作者
STOLLE, CA
PYERITZ, RE
MYERS, JC
PROCKOP, DJ
机构
[1] UNIV MED & DENT NEW JERSEY, RUTGERS MED SCH, DEPT BIOCHEM, PISCATAWAY, NJ 08854 USA
[2] JOHNS HOPKINS UNIV, SCH MED, DEPT MED, BALTIMORE, MD 21205 USA
[3] JOHNS HOPKINS UNIV, SCH MED, DEPT PEDIAT, BALTIMORE, MD 21205 USA
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D O I
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中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
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页码:1937 / 1944
页数:8
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