EMERGENCY OPERATION FOR THORACIC AORTIC-ANEURYSM CAUSED BY THE EHLERS-DANLOS SYNDROME

被引:10
|
作者
HAMANO, K
MINAMI, Y
FUJIMURA, Y
TSUBOI, H
FURUKAWA, S
ODA, T
ESATO, K
机构
[1] First Department of Surgery, Yamaguchi University School of Medicine, Department of Surgery, Yamaguchi
来源
ANNALS OF THORACIC SURGERY | 1994年 / 58卷 / 04期
关键词
D O I
10.1016/0003-4975(94)90488-X
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Two patients were treated emergently for impending ruptured thoracic aortic aneurysms caused by type IV Ehlers-Danlos syndrome. One patient had typical physical evidence of type IV Ehlers-Danlos syndrome. The other patient had a normal phenotype. Type IV Ehlers-Danlos syndrome was diagnosed by electrophoresis of the collagen extracted from the skin. The clinician must be aware of the variations in presentation of type IV Ehlers-Danlos syndrome.
引用
收藏
页码:1180 / 1182
页数:3
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