WEGENER GRANULOMATOSIS WITH EXCLUSIVE RENAL INVOLVEMENT

被引:0
|
作者
MAZUECOS, A [1 ]
ANDRES, A [1 ]
SANCHEZ, R [1 ]
ARAQUE, A [1 ]
VILLENA, MV [1 ]
DEPRADA, I [1 ]
USERA, G [1 ]
PRAGA, M [1 ]
机构
[1] HOSP OCTUBRE 12,SERV NEFROL,CTRA ANDALUCIA,KM 5 450,MADRID,SPAIN
来源
NEFROLOGIA | 1994年 / 14卷 / 03期
关键词
WEGENER GRANULOMATOSIS; ACUTE RENAL FAILURE; HEMODIALYSIS; PERIGLOMERULAR GRANULOMATOSIS; ANCA;
D O I
暂无
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Cases of Wegener's granulomatosis with exclusive renal involvement are very unusual. Here we report a patient who presented which acute renal failure with massive extracapillary proliferation on renal biopsy, without extrarenal manifestations. After 9 years on chronic hemodialysis she developed several otorhinological abnormalities and finally pulmonary nodes. Lung biopsy showed a granulomatous vasculitis characteristic of Wegener's granulomatosis. Wegener's disease can recur after prolonged asymptomatic periods. In those cases with exclusive renal involvement, diagnosis can be delayed until the appearance of respiratory manifestations.
引用
收藏
页码:345 / 350
页数:6
相关论文
共 50 条
  • [31] WEGENER GRANULOMATOSIS WITH AN AORTA VALVE INVOLVEMENT
    TIMOSHENKO, VS
    POLUSHIN, OG
    FISENKO, AI
    [J]. ARKHIV PATOLOGII, 1989, 51 (12) : 55 - 58
  • [32] SELECTIVE RENAL ANGIOGRAPHY IN WEGENER GRANULOMATOSIS
    MOUTSOPOULOS, HM
    AVGERINOS, PC
    TSAMPOULAS, CG
    KATSIOTIS, PA
    [J]. ANNALS OF THE RHEUMATIC DISEASES, 1983, 42 (02) : 192 - 195
  • [33] Renal relapse in Wegener’s granulomatosis
    Luis R. Espinoza
    [J]. Current Rheumatology Reports, 2003, 5 (2) : 91 - 92
  • [34] Renal Limited Wegener's granulomatosis
    Del Porto, F.
    Proietta, M.
    Stoppacciaro, A.
    Trappolini, M.
    Mene, P.
    Aliberti, G.
    [J]. LUPUS, 2009, 18 (06) : 567 - 569
  • [35] RENAL-TRANSPLANTATION IN WEGENER GRANULOMATOSIS
    SCHMITT, WH
    HAUBITZ, M
    MISTRY, N
    BRUNKHORST, R
    ERBSLOHMOLLER, B
    GROSS, WL
    [J]. LANCET, 1993, 342 (8875): : 860 - 860
  • [36] Wegener's granulomatosis with granulomatous liver involvement
    Holl-Ulrich, K.
    Klass, M.
    [J]. CLINICAL AND EXPERIMENTAL RHEUMATOLOGY, 2010, 28 (01) : S88 - S89
  • [37] Cardiac involvement in Wegener granulomatosis diagnosed at autopsy
    Mukhopadhyay, Sanjay
    Hensley, Richard G.
    Tazelaar, Henry D.
    [J]. CARDIOVASCULAR PATHOLOGY, 2010, 19 (05) : 312 - 315
  • [38] Bilateral parotid gland involvement in Wegener granulomatosis
    Saha, A. K.
    Rachapalli, S.
    Steer, S.
    Gordon, P.
    [J]. ANNALS OF THE RHEUMATIC DISEASES, 2009, 68 (07) : 1233 - 1234
  • [39] WEGENER GRANULOMATOSIS PRESENTING AS RENAL MASS
    SCHAPIRA, HE
    KAPNER, J
    SZPORN, AH
    [J]. UROLOGY, 1986, 28 (04) : 307 - 309
  • [40] Pulmonary artery involvement in Wegener's granulomatosis
    Clark, T
    Hoffman, GS
    [J]. CLINICAL AND EXPERIMENTAL RHEUMATOLOGY, 2003, 21 (06) : S124 - S126