Atypical hemolytic uremic syndrome. Case report and review of the literature

被引:0
|
作者
Jimenez-Garcia, Raquel [1 ]
Rebolledo-Zamora, Alejandra [2 ]
Mayela Vazquez-Perdomo, Maria del Rosario [3 ]
Bojorquez-Ochoa, Aurora [1 ]
Tomas Corcuera-Delgado, Celso [4 ]
机构
[1] Inst Nacl Pediat, Dept Nefrol Pediat, Ciudad De Mexico, Mexico
[2] Inst Nacl Pediat, Nefrol Pediat, Ciudad De Mexico, Mexico
[3] Inst Nacl Pediat, Pediat, Ciudad De Mexico, Mexico
[4] Inst Nacl Pediat, Dept Anat Patol, Ciudad De Mexico, Mexico
来源
ACTA PEDIATRICA DE MEXICO | 2018年 / 39卷 / 03期
关键词
atypical hemolytic uremic syndrome; thrombotic microangiopathy; eculizumab;
D O I
10.18233/APM39No3pp250-2551609
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
INTRODUCTION : The hemolytic uremic syndrome in its atypical variety is a rare thrombotic microangiopathy, with high morbidity and mortality if a timely diagnosis is not available to allow an adequate specific treatment. CLINICAL CASE: Patient with a confirmed diagnosis of atypical hemolytic uremic syndrome treated with eculizumah with total remission and satisfactory clinical evolution. Diagnostic suspicion is important for early and specific treatment and favorable prognosis. CONCLUSION: The case reported here is illustrative of the clinical presentation of the atypical haemolytic uraemic syndrome. Its evolution was torpid, despite the treatment with plasma infusion and plasmapheresis and its total remission with eculizumab. In Mexico, few cases have been confirmed, only in some cases has the specific treatment been administered.
引用
收藏
页码:250 / 255
页数:6
相关论文
共 50 条
  • [21] Simultaneous occurrence of atypical hemolytic uremic syndrome and acute lymphoblastic leukemia: a case report and literature review
    Rajiv Sinha
    Abdullah AlAbbas
    Janis M. Dionne
    Robert Morrison Hurley
    Pediatric Nephrology, 2008, 23 : 835 - 839
  • [22] Maintenance eculizumab dose adjustment in the treatment of atypical hemolytic uremic syndrome: a case report and review of the literature
    Thomson, Nick
    Ulrickson, Matthew
    CLINICAL CASE REPORTS, 2016, 4 (08): : 773 - 776
  • [23] Atypical hemolytic uremic syndrome induced by CblC subtype of methylmalonic academia: A case report and literature review
    Chen, Minguang
    Zhuang, Jieqiu
    Yang, JianHuan
    Wang, Dexuan
    Yang, Qing
    MEDICINE, 2017, 96 (43)
  • [24] Atypical hemolytic uremic syndrome. Report of two cases treated with Eculizumab
    Tagle, Rodrigo
    Rivera, Gustavo
    Walbaum, Benjamin
    Sepulveda, Rodrigo A.
    REVISTA MEDICA DE CHILE, 2018, 146 (02) : 254 - 259
  • [25] Early gestational hemolytic uremic syndrome: Case report and review of literature
    Ribeiro, FM
    Rocha, E
    Maccariello, E
    Caldas, LR
    Gomes, MV
    Lugon, JR
    RENAL FAILURE, 1997, 19 (03) : 475 - 479
  • [26] Epidemiology of Atypical Hemolytic Uremic Syndrome: A Systematic Literature Review
    Yan, Kevin
    Desai, Kamal
    Gullapalli, Lakshmi
    Druyts, Eric
    Balijepalli, Chakrapani
    CLINICAL EPIDEMIOLOGY, 2020, 12 : 295 - 305
  • [27] Atypical Lemierre's Syndrome. A Case Report and Review of Literature
    Qureshi, Anum
    Bailey, Theodore
    Atkinson, Michael
    Tayabali, Khadija
    JOURNAL OF COMMUNITY HOSPITAL INTERNAL MEDICINE PERSPECTIVES, 2022, 12 (01): : 36 - 38
  • [28] AN ATYPICAL CASE OF ATYPICAL HEMOLYTIC UREMIC SYNDROME
    Srivastava, Romik
    Avery, Alexandria
    Schumann, Samuel O.
    JOURNAL OF GENERAL INTERNAL MEDICINE, 2020, 35 (SUPPL 1) : S376 - S376
  • [29] An Atypical Case of Atypical Hemolytic Uremic Syndrome
    Francois, Tine
    Vande Walle, Johan
    Dhont, Evelyn
    Keenswijk, Werner
    JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY, 2019, 41 (02) : E111 - E113
  • [30] ATYPICAL CASE OF ATYPICAL HEMOLYTIC UREMIC SYNDROME
    Pomerants, Sarah
    Tosado, Michelle Hornedo
    Graef, Andrew
    CHEST, 2024, 166 (04) : 2564A - 2565A