MYOPATHY DUE TO GLYCOGEN-STORAGE DISEASE - PATHOLOGICAL AND BIOCHEMICAL-STUDIES IN RELATION TO GLYCOGENOSOME FORMATION

被引:25
|
作者
IWAMASA, T
FUKUDA, S
TOKUMITSU, S
NINOMIYA, N
MATSUDA, I
OSAME, M
机构
[1] KUMAMOTO UNIV, SCH MED, DEPT PEDIAT, KUMAMOTO 860, JAPAN
[2] KAGOSHIMA UNIV, SCH MED, DEPT BUNKYO KU, KAGOSHIMA 890, JAPAN
关键词
D O I
10.1016/0014-4800(83)90080-1
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
引用
收藏
页码:405 / 420
页数:16
相关论文
共 50 条
  • [21] PORTAL DIVERSION IN GLYCOGEN-STORAGE DISEASE (GSD) - STUDIES IN 11 CASES
    ODIEVRE, M
    BISMUTH, H
    DOUILLET, P
    MOATTI, N
    BRIVET, M
    BAUSSAN, C
    PEDIATRIC RESEARCH, 1980, 14 (02) : 169 - 169
  • [22] INFANTILE SIALIC-ACID STORAGE DISEASE - BIOCHEMICAL-STUDIES
    BERRA, B
    GORNATI, R
    RAPELLI, S
    GATTI, R
    MANCINI, GMS
    CIANA, G
    BEMBI, B
    AMERICAN JOURNAL OF MEDICAL GENETICS, 1995, 58 (01): : 24 - 31
  • [23] GLYCOPROTEIN STORAGE IN GAUCHER DISEASE - LECTIN HISTOCHEMISTRY AND BIOCHEMICAL-STUDIES
    DEGASPERI, R
    ALROY, J
    RICHARD, R
    GOYAL, V
    ORGAD, U
    LEE, RE
    WARREN, CD
    LABORATORY INVESTIGATION, 1990, 63 (03) : 385 - 393
  • [24] MECHANIC FORMATION OF GLYCOGENOSOME .3. PHYSIOCHEMICAL AND ULTRASTRUCTURAL STUDIES OF GLYCOGEN EXTRACTED FROM POMPES DISEASE
    IWAMASA, T
    TSURU, T
    HAMADA, T
    TAKEUCHI, T
    ACTA HISTOCHEMICA ET CYTOCHEMICA, 1978, 11 (01) : 117 - 117
  • [25] ADULT MYOPATHY FROM GLYCOGEN STORAGE DISEASE DUE TO ACID MALTASE DEFICIENCY
    HUDGSON, P
    GARDNERM.D
    WORSFOLD, M
    PENNINGTON, RJ
    WALTON, JN
    BRAIN, 1968, 91 : 435 - +
  • [26] ULTRASTRUCTURE STUDIES ON LIVER AND PERIPHERAL-BLOOD IN 2 SIBLING WITH GLYCOGEN-STORAGE DISEASE
    ADACHI, H
    ISHIHARA, T
    UCHINO, F
    JOURNAL OF ELECTRON MICROSCOPY, 1974, 23 (01): : 75 - 75
  • [27] BIOCHEMICAL STUDIES AND SPECIFIC THERAPY IN HEPATIC GLYCOGEN STORAGE DISEASE
    LOWE, CU
    SOKAL, JE
    DORAY, BH
    SARCIONE, EJ
    JOURNAL OF CLINICAL INVESTIGATION, 1959, 38 (06): : 1021 - 1022
  • [28] CARDIAC INVOLVEMENT IN GLYCOGEN-STORAGE DISEASE .3. MORPHOLOGIC AND BIOCHEMICAL-CHARACTERIZATION WITH ENDOMYOCARDIAL BIOPSY
    OLSON, LJ
    REEDER, GS
    NOLLER, KL
    EDWARDS, WD
    HOWELL, RR
    MICHELS, VV
    AMERICAN JOURNAL OF CARDIOLOGY, 1984, 53 (07): : 980 - 981
  • [29] CASE OF GLYCOGEN-STORAGE DISEASE DUE TO LIVER AND MUSCLE PHOSPHORYLASE-B KINASE-DEFICIENCY
    BASHAN, N
    GORODISCHER, R
    IANCU, PC
    LERNER, A
    MOSES, S
    PEDIATRIC RESEARCH, 1979, 13 (04) : 367 - 367
  • [30] AN ADULT CASE OF TYPE-IB GLYCOGEN-STORAGE DISEASE - ENZYMATIC AND HISTOCHEMICAL-STUDIES
    KUZUYA, T
    MATSUDA, A
    YOSHIDA, S
    NARISAWA, K
    TADA, K
    SAITO, T
    MATSUSHITA, M
    NEW ENGLAND JOURNAL OF MEDICINE, 1983, 308 (10): : 566 - 569