ATRIOVENTRICULAR-BLOCK AND DISTAL MYOPATHY WITH RIMMED VACUOLES AND DESMIN STORAGE

被引：0

作者：

TELERMANTOPPET, N ^{[1
]}

BAUHERZ, G ^{[1
]}

NOEL, S ^{[1
]}

机构：

[1] UNIV LIBRE BRUXELLES,MOLIERE HOSP,DEPT NEUROL,B-1050 BRUSSELS,BELGIUM

来源：

CLINICAL NEUROPATHOLOGY | 1991年 / 10卷 / 02期

关键词：

AV BLOCK; DESMIN; INCLUSION BODY MYOSITIS; RIMMED VACUOLES;

D O I：

暂无

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

A young patient had an auriculo-ventricular block and a distal myopathy with muscle biopsy findings suggestive of inclusion body myositis. What was most unusual was the presence of numerous sarcoplasmic bodies identified as desmin by electron microscopy and immunocytochemistry. The nosological situation of this condition is discussed.

引用

页码：61 / 64

页数：4

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