Congenital absence of the portal vein in a boy

被引:0
|
作者
E. Kohda
Morihiro Saeki
Miwako Nakano
Hidekazu Masaki
Kenji Ogawa
Mali Nirasawa
K. Hiramatsu
机构
[1] Department of Radiology,
[2] Keio University School of Medicine,undefined
[3] Shinanomachi 35,undefined
[4] Shinjuku-ku,undefined
[5] Tokyo 1608582,undefined
[6] Japan,undefined
[7] Department of Radiology and Surgery,undefined
[8] National Children Hospital,undefined
[9] Tokyo,undefined
[10] Japan,undefined
[11] Department of Radiology and Paediatrics,undefined
[12] Nihon Kohkan Hospital,undefined
[13] Kawasaki,undefined
[14] Japan,undefined
来源
Pediatric Radiology | 1999年 / 29卷
关键词
Female Patient; Portal Vein; Congenital Abnormality; Male Patient; Liver Tumour;
D O I
暂无
中图分类号
学科分类号
摘要
Congenital absence of the portal vein (CAPV) is a malformation that is generally thought to be limited to females. We encountered an 11-year-old boy with this malformation. In 17 previously reported cases of CAPV, 2 were male. Three male patients, including our case, were Abernethy type Ib malformation. They had no associated liver tumour and two had no additional congenital abnormality. Conversely, 13 of the 15 female patients had congenital abnormalities and 6 had liver mass lesions.
引用
收藏
页码:235 / 237
页数:2
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